Sequence of the FRA3B common fragile region: implications for the mechanism of FHIT deletion

Proc Natl Acad Sci U S A. 1997 Dec 23;94(26):14584-9. doi: 10.1073/pnas.94.26.14584.

Abstract

The hypothesis that chromosomal fragile sites may be "weak links" that result in hot spots for cancer-specific chromosome rearrangements was supported by the discovery that numerous cancer cell homozygous deletions and a familial translocation map within the FHIT gene, which encompasses the common fragile site, FRA3B. Sequence analysis of 276 kb of the FRA3B/FHIT locus and 22 associated cancer cell deletion endpoints shows that this locus is a frequent target of homologous recombination between long interspersed nuclear element sequences resulting in FHIT gene internal deletions, probably as a result of carcinogen-induced damage at FRA3B fragile sites.

Publication types

  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Acid Anhydride Hydrolases*
  • Chromosome Fragile Sites
  • Chromosome Fragility*
  • Gene Deletion*
  • Humans
  • Molecular Sequence Data
  • Neoplasm Proteins*
  • Proteins / genetics*
  • Recombination, Genetic*
  • Tumor Cells, Cultured

Substances

  • Neoplasm Proteins
  • Proteins
  • fragile histidine triad protein
  • Acid Anhydride Hydrolases

Associated data

  • GENBANK/AF019967
  • GENBANK/AF020503
  • GENBANK/AF020504
  • GENBANK/AF020609
  • GENBANK/AF020610
  • GENBANK/AF020611
  • GENBANK/AF020612
  • GENBANK/AF020613
  • GENBANK/AF020614
  • GENBANK/AF020615