Alpha2-macroglobulin attenuates beta-amyloid peptide 1-40 fibril formation and associated neurotoxicity of cultured fetal rat cortical neurons

J Neurochem. 1998 Mar;70(3):1182-8. doi: 10.1046/j.1471-4159.1998.70031182.x.

Abstract

Beta-amyloid peptides (A beta) are deposited in an aggregated fibrillar form in both diffuse and senile plaques in the brains of patients with Alzheimer's disease. The neurotoxicity of A beta in cultured neurons is dependent on its aggregation state, but the factors contributing to aggregation and fibril formation are poorly understood. In the present study, we investigated whether alpha2-macroglobulin (alpha2M), a protein present in neuritic plaques and elevated in Alzheimer's disease brain, is a potential regulatory factor for A beta fibril formation. Previous studies in our laboratory have shown that alpha2M is an A beta binding protein. We now report that, in contrast to another plaque-associated protein, alpha1-antichymotrypsin, alpha2M coincubated with A beta significantly reduces aggregation and fibril formation in vitro. Additionally, cultured fetal rat cortical neurons are less vulnerable to the toxic actions of aged A beta following pretreatment with alpha2M. We postulate that alpha2M is able to maintain A beta in a soluble state, preventing fibril formation and associated neurotoxicity.

MeSH terms

  • Alzheimer Disease / metabolism
  • Amyloid beta-Peptides / metabolism*
  • Animals
  • Cells, Cultured
  • Cerebral Cortex / cytology*
  • Endocytosis
  • Endopeptidases / metabolism
  • Neurons / cytology
  • Neurons / drug effects*
  • Neurons / enzymology
  • Neurotoxins / pharmacology
  • Peptide Fragments / metabolism*
  • Rats
  • Rats, Sprague-Dawley
  • Serine Proteinase Inhibitors / pharmacology
  • alpha 1-Antichymotrypsin / pharmacology
  • alpha-Macroglobulins / pharmacology*

Substances

  • Amyloid beta-Peptides
  • Neurotoxins
  • Peptide Fragments
  • Serine Proteinase Inhibitors
  • alpha 1-Antichymotrypsin
  • alpha-Macroglobulins
  • amyloid beta-protein (1-40)
  • Endopeptidases