HLA antigens and pANCA define ulcerative colitis as a genetically heterogeneous disorder

Ital J Gastroenterol Hepatol. 1998 Feb;30(1):56-61.

Abstract

Background: Several genetic and subclinical markers have been associated with ulcerative colitis.

Aim: To determine whether a significant association with HLA class I and II antigens was present in Italian ulcerative colitis patients considered as a whole population or stratified according to their anti-neutrophil cytoplasmatic antibodies.

Methods: HLA class I and II antigens were studied by serological typing techniques and related to the presence of anti-neutrophil cytoplasmatic antibodies detected by means of indirect immunofluorescence.

Results: Patients with ulcerative colitis (n = 45) had a significantly increased frequency of DQ6 (p = 0.04) and DQ7 (p = 0.003) and a decreased frequency of DQ5 (p = 0.03) and DQ8 (p = 0.02) when compared with ethnically matched healthy controls (n = 252 for HLA class I and 173 for HLA class II). No significant difference in HLA I- and DR-antigens was observed. Anti-neutrophil cytoplasmatic antibodies were found in 27/45 (60%) ulcerative colitis patients and in 0/252 controls (p < 0.001). After stratifying ulcerative colitis patients according to their anti-neutrophil cytoplasmatic antibodies status, anti-neutrophil cytoplasmatic antibodies +ve patients had an increased frequency of A19 (p = 0.007), DR2 (p = 0.03), and DR15 (p = 0.006), and a decreased frequency of A1 (p = 0.004) compared with anti-neutrophil cytoplasmatic antibodies -ve ones.

Conclusions: We suggest that specific HLA-class II loci play an important role in the susceptibility to ulcerative colitis in Italy. A subset of ulcerative colitis patients is characterised by the presence of a specific subclinical marker (anti-neutrophil cytoplasmatic antibodies) which seems to be genetically determined as shown by the increased frequencies of HLA-A19 and DR2 observed in anti-neutrophil cytoplasmatic antibodies +ve ulcerative colitis.

Publication types

  • Comparative Study

MeSH terms

  • Adult
  • Antibodies, Antineutrophil Cytoplasmic / immunology*
  • Colitis, Ulcerative / epidemiology
  • Colitis, Ulcerative / genetics*
  • Colitis, Ulcerative / immunology
  • Female
  • Fluorescent Antibody Technique, Indirect
  • Heterozygote
  • Histocompatibility Antigens Class I / genetics*
  • Histocompatibility Antigens Class II / genetics*
  • Histocompatibility Testing
  • Humans
  • Italy / epidemiology
  • Linkage Disequilibrium
  • Male
  • Neutrophils / immunology
  • Prevalence

Substances

  • Antibodies, Antineutrophil Cytoplasmic
  • Histocompatibility Antigens Class I
  • Histocompatibility Antigens Class II