Fenestration of extracardiac fontan and reversal of protein-losing enteropathy: case report

V Lemes; A M Murphy; F A Osterman; J C Laschinger; J S Kan

doi:10.1007/s002469900322

Fenestration of extracardiac fontan and reversal of protein-losing enteropathy: case report

Pediatr Cardiol. 1998 Jul-Aug;19(4):355-7. doi: 10.1007/s002469900322.

Authors

V Lemes¹, A M Murphy, F A Osterman, J C Laschinger, J S Kan

Affiliation

¹ Department of Pediatrics, Division of Pediatric Cardiology, The Johns Hopkins Hospital, 600 North Wolfe Street, Brady 5, Baltimore, MD 21287, USA.

PMID: 9636262
DOI: 10.1007/s002469900322

Abstract

We describe a patient with protein-losing enteropathy who presented 6 months after undergoing a modified Fontan operation. After failing to respond to medical therapy, the Fontan tunnel was fenestrated by catheter intervention with immediate improvement and resolution of hypoproteinemia and enteric protein loss.

Publication types

Case Reports

MeSH terms

Angiography
Cardiac Catheterization
Child, Preschool
Echocardiography, Transesophageal
Follow-Up Studies
Fontan Procedure / adverse effects*
Heart Defects, Congenital / diagnosis
Heart Defects, Congenital / surgery*
Humans
Male
Postoperative Complications / diagnosis
Postoperative Complications / etiology*
Postoperative Complications / surgery
Protein-Losing Enteropathies / etiology*
Pulmonary Artery / diagnostic imaging
Reoperation