Neurofibromatosis type 1 associated with systemic vasculopathy

Eur J Dermatol. 1998 Jun;8(4):271-3.

Abstract

Systemic vasculopathy in patients with neurofibromatosis type 1 is rare. We describe a case of unusual cerebral and renal involvement in a young, 29-year-old patient, who died of a cerebral ischemic attack one year after our observation.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Angiography
  • Aorta, Abdominal / diagnostic imaging
  • Aorta, Abdominal / pathology
  • Brain Ischemia / diagnosis
  • Brain Ischemia / etiology*
  • Fatal Outcome
  • Female
  • Humans
  • Hypertension, Renal / diagnosis
  • Hypertension, Renal / etiology*
  • Neurofibromatosis 1 / complications*
  • Tomography, X-Ray Computed