Abstract
Two cases of Papillon-Lefèvre syndrome, a rare hereditary affection of unknown etiology, whose clinical signs are hyperkeratosis palmoplantaris and parodontitis, are described. The results obtained with the ultrastructural examination of the lesions are shown. A therapeutic protocol which can reduce the evolution of the pathology, is also suggested.
Publication types
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Case Reports
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English Abstract
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Review
MeSH terms
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Adult
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Combined Modality Therapy
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Desmosomes / ultrastructure
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Female
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Foot / pathology
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Gingiva / ultrastructure
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Hand / pathology
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Humans
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Male
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Mouth, Edentulous / pathology
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Papillon-Lefevre Disease / diagnosis*
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Papillon-Lefevre Disease / pathology
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Papillon-Lefevre Disease / therapy
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Skin / ultrastructure
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Tooth Mobility / pathology