Total body irradiation, cyclophosphamide, and etoposide with stem cell transplant as treatment for infants with acute lymphocytic leukemia

Med Pediatr Oncol. 1999 Jan;32(1):1-6. doi: 10.1002/(sici)1096-911x(199901)32:1<1::aid-mpo2>3.0.co;2-j.

Abstract

Background: Acute lymphoblastic leukemia (ALL) in infants has a very poor outcome with modern chemotherapy. We reviewed our experience with the infants diagnosed with ALL at Children's Memorial Hospital from 1992 to 1997.

Procedure: During this time period, 10 infants were diagnosed with ALL. Seven of them were transplanted, four with marrow from HLA-matched siblings and three with umbilical cord blood. Four of the transplanted patients had the MLL gene rearrangement and the other three transplanted patients had one or more other high-risk features including CD10-blasts, age less than 6 months at diagnosis, or prior relapse. The patients were conditioned with a regimen of total body irradiation (TBI), etoposide, and cyclophosphamide (CY). Peritransplant toxicity was tolerable. The graft infused contained a median total nucleated cell dose/kg of 3 x 10(8) (.3 x 10(8)-6 x 10(8)). The median CD34+ cell dose/kg was 5 x 10(6) (.25 x 10(6)-31 x 10(6)).

Results: All of the patients engrafted with a median of 18 days (11-29) to reach an absolute neutrophil count (ANC) of 500/microliter. The median time to reach an unsupported platelet count greater than 20,000/microliter was 24 days (18-64). Four of seven of the transplanted patients are leukemia-free survivors at a median follow-up of 775 days. Of the three patients who were not transplanted, one is surviving 2+ years off therapy.

Conclusions: Allogeneic stem cell transplant is an alternative to chemotherapy alone as a treatment for infant ALL when a suitable donor is available.

MeSH terms

  • Age Factors
  • Antigens, CD34 / analysis
  • Antineoplastic Agents, Alkylating / administration & dosage*
  • Antineoplastic Agents, Phytogenic / administration & dosage*
  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use*
  • Bone Marrow Transplantation*
  • Cyclophosphamide / administration & dosage*
  • Disease-Free Survival
  • Etoposide / administration & dosage*
  • Female
  • Fetal Blood
  • Follow-Up Studies
  • Gene Rearrangement
  • HLA Antigens
  • Hematopoietic Stem Cell Transplantation*
  • Histocompatibility
  • Humans
  • Infant
  • Leukocyte Count
  • Male
  • Neoplasm Recurrence, Local / pathology
  • Neprilysin / analysis
  • Neutrophils / pathology
  • Platelet Count
  • Precursor Cell Lymphoblastic Leukemia-Lymphoma / therapy*
  • Risk Factors
  • Transplantation Conditioning
  • Treatment Outcome
  • Whole-Body Irradiation*

Substances

  • Antigens, CD34
  • Antineoplastic Agents, Alkylating
  • Antineoplastic Agents, Phytogenic
  • HLA Antigens
  • Etoposide
  • Cyclophosphamide
  • Neprilysin