Strauss AW - Search Results

1

Inborn errors of mitochondrial fatty acid oxidation.

Bennett MJ, Rinaldo P, Strauss AW. Bennett MJ, et al. Among authors: strauss aw. Crit Rev Clin Lab Sci. 2000 Feb;37(1):1-44. doi: 10.1080/10408360091174169. Crit Rev Clin Lab Sci. 2000. PMID: 10737439 Review.

2

Intact alpha-subunit is required for membrane-binding of human mitochondrial trifunctional beta-oxidation protein, but is not necessary for conferring 3-ketoacyl-CoA thiolase activity to the beta-subunit.

Weinberger MJ, Rinaldo P, Strauss AW, Bennett MJ. Weinberger MJ, et al. Among authors: strauss aw. Biochem Biophys Res Commun. 1995 Apr 6;209(1):47-52. doi: 10.1006/bbrc.1995.1468. Biochem Biophys Res Commun. 1995. PMID: 7726862 Free article.

3

Human placenta metabolizes fatty acids: implications for fetal fatty acid oxidation disorders and maternal liver diseases.

Shekhawat P, Bennett MJ, Sadovsky Y, Nelson DM, Rakheja D, Strauss AW. Shekhawat P, et al. Among authors: strauss aw. Am J Physiol Endocrinol Metab. 2003 Jun;284(6):E1098-105. doi: 10.1152/ajpendo.00481.2002. Epub 2003 Feb 11. Am J Physiol Endocrinol Metab. 2003. PMID: 12582009 Free article.

4

A fetal fatty-acid oxidation disorder as a cause of liver disease in pregnant women.

Ibdah JA, Bennett MJ, Rinaldo P, Zhao Y, Gibson B, Sims HF, Strauss AW. Ibdah JA, et al. Among authors: strauss aw. N Engl J Med. 1999 Jun 3;340(22):1723-31. doi: 10.1056/NEJM199906033402204. N Engl J Med. 1999. PMID: 10352164 Free article.

5

Accumulation of free 3-hydroxy fatty acids in the culture media of fibroblasts from patients deficient in long-chain l-3-hydroxyacyl-CoA dehydrogenase: a useful diagnostic aid.

Jones PM, Moffitt M, Joseph D, Harthcock PA, Boriack RL, Ibdah JA, Strauss AW, Bennett MJ. Jones PM, et al. Among authors: strauss aw. Clin Chem. 2001;47(7):1190-4. Clin Chem. 2001. PMID: 11427448

6

Mutations in long-chain 3-hydroxyacyl coenzyme a dehydrogenase are associated with placental maternal floor infarction/massive perivillous fibrin deposition.

Griffin AC, Strauss AW, Bennett MJ, Ernst LM. Griffin AC, et al. Among authors: strauss aw. Pediatr Dev Pathol. 2012 Sep-Oct;15(5):368-74. doi: 10.2350/12-05-1198-OA.1. Epub 2012 Jul 2. Pediatr Dev Pathol. 2012. PMID: 22746996

7

Early neonatal diagnosis of long-chain 3-hydroxyacyl coenzyme a dehydrogenase and mitochondrial trifunctional protein deficiencies.

Hintz SR, Matern D, Strauss A, Bennett MJ, Hoyme HE, Schelley S, Kobori J, Colby C, Lehman NL, Enns GM. Hintz SR, et al. Mol Genet Metab. 2002 Feb;75(2):120-7. doi: 10.1006/mgme.2001.3282. Mol Genet Metab. 2002. PMID: 11855930

8

Molecular prenatal diagnosis in families with fetal mitochondrial trifunctional protein mutations.

Ibdah JA, Zhao Y, Viola J, Gibson B, Bennett MJ, Strauss AW. Ibdah JA, et al. Among authors: strauss aw. J Pediatr. 2001 Mar;138(3):396-9. doi: 10.1067/mpd.2001.111503. J Pediatr. 2001. PMID: 11241049

9

The molecular basis of pediatric long chain 3-hydroxyacyl-CoA dehydrogenase deficiency associated with maternal acute fatty liver of pregnancy.

Sims HF, Brackett JC, Powell CK, Treem WR, Hale DE, Bennett MJ, Gibson B, Shapiro S, Strauss AW. Sims HF, et al. Among authors: strauss aw. Proc Natl Acad Sci U S A. 1995 Jan 31;92(3):841-5. doi: 10.1073/pnas.92.3.841. Proc Natl Acad Sci U S A. 1995. PMID: 7846063 Free PMC article.

10

Placental floor infarction complicating the pregnancy of a fetus with long-chain 3-hydroxyacyl-CoA dehydrogenase (LCHAD) deficiency.

Matern D, Schehata BM, Shekhawa P, Strauss AW, Bennett MJ, Rinaldo P. Matern D, et al. Among authors: strauss aw. Mol Genet Metab. 2001 Mar;72(3):265-8. doi: 10.1006/mgme.2000.3135. Mol Genet Metab. 2001. PMID: 11243734

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