Paul HS - Search Results

1

Hepatocyte transplantation (HTx) corrects selected neurometabolic abnormalities in murine intermediate maple syrup urine disease (iMSUD).

Skvorak KJ, Hager EJ, Arning E, Bottiglieri T, Paul HS, Strom SC, Homanics GE, Sun Q, Jansen EE, Jakobs C, Zinnanti WJ, Gibson KM. Skvorak KJ, et al. Among authors: paul hs. Biochim Biophys Acta. 2009 Oct;1792(10):1004-10. doi: 10.1016/j.bbadis.2009.08.006. Epub 2009 Aug 19. Biochim Biophys Acta. 2009. PMID: 19699299 Free PMC article.

2

Production and characterization of murine models of classic and intermediate maple syrup urine disease.

Homanics GE, Skvorak K, Ferguson C, Watkins S, Paul HS. Homanics GE, et al. Among authors: paul hs. BMC Med Genet. 2006 Mar 31;7:33. doi: 10.1186/1471-2350-7-33. BMC Med Genet. 2006. PMID: 16579849 Free PMC article.

3

Hepatocyte transplantation improves phenotype and extends survival in a murine model of intermediate maple syrup urine disease.

Skvorak KJ, Paul HS, Dorko K, Marongiu F, Ellis E, Chace D, Ferguson C, Gibson KM, Homanics GE, Strom SC. Skvorak KJ, et al. Among authors: paul hs. Mol Ther. 2009 Jul;17(7):1266-73. doi: 10.1038/mt.2009.99. Epub 2009 May 12. Mol Ther. 2009. PMID: 19436271 Free PMC article.

4

Dual mechanism of brain injury and novel treatment strategy in maple syrup urine disease.

Zinnanti WJ, Lazovic J, Griffin K, Skvorak KJ, Paul HS, Homanics GE, Bewley MC, Cheng KC, Lanoue KF, Flanagan JM. Zinnanti WJ, et al. Among authors: paul hs. Brain. 2009 Apr;132(Pt 4):903-18. doi: 10.1093/brain/awp024. Epub 2009 Mar 17. Brain. 2009. PMID: 19293241 Free PMC article.

5

Complementation of defective leucine decarboxylation in fibroblasts from a maple syrup urine disease patient by retrovirus-mediated gene transfer.

Mueller GM, McKenzie LR, Homanics GE, Watkins SC, Robbins PD, Paul HS. Mueller GM, et al. Among authors: paul hs. Gene Ther. 1995 Sep;2(7):461-8. Gene Ther. 1995. PMID: 7584124

6

Inhibition of carnitine acyltransferase activities by bile acids in rat liver peroxisomes.

Sekas G, Paul HS. Sekas G, et al. Among authors: paul hs. Biochim Biophys Acta. 1992 Apr 23;1125(2):196-202. doi: 10.1016/0005-2760(92)90045-w. Biochim Biophys Acta. 1992. PMID: 1571363

7

Investigation of the presence of branched-chain alpha-keto acid dehydrogenase in mammalian hepatic peroxisomes.

Paul HS, Sekas G, Adibi SA. Paul HS, et al. Int J Biochem. 1992 Apr;24(4):617-9. doi: 10.1016/0020-711x(92)90336-y. Int J Biochem. 1992. PMID: 1516734

8

Hepatic release of carnitine: effect of increased concentration by clofibrate treatment.

Paul HS, Sekas G. Paul HS, et al. Biochem Med Metab Biol. 1992 Feb;47(1):21-30. doi: 10.1016/0885-4505(92)90004-i. Biochem Med Metab Biol. 1992. PMID: 1562353

9

Carnitine biosynthesis in hepatic peroxisomes. Demonstration of gamma-butyrobetaine hydroxylase activity.

Paul HS, Sekas G, Adibi SA. Paul HS, et al. Eur J Biochem. 1992 Feb 1;203(3):599-605. doi: 10.1111/j.1432-1033.1992.tb16589.x. Eur J Biochem. 1992. PMID: 1735445 Free article.

10

Inhibition of carnitine acetyltransferase by bile acids: implications for carnitine analysis.

Sekas G, Paul HS. Sekas G, et al. Among authors: paul hs. Anal Biochem. 1989 Jun;179(2):262-7. doi: 10.1016/0003-2697(89)90125-5. Anal Biochem. 1989. PMID: 2774175

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