Flanagan-Steet H - Search Results

1

A zebrafish model of PMM2-CDG reveals altered neurogenesis and a substrate-accumulation mechanism for N-linked glycosylation deficiency.

Cline A, Gao N, Flanagan-Steet H, Sharma V, Rosa S, Sonon R, Azadi P, Sadler KC, Freeze HH, Lehrman MA, Steet R. Cline A, et al. Mol Biol Cell. 2012 Nov;23(21):4175-87. doi: 10.1091/mbc.E12-05-0411. Epub 2012 Sep 5. Mol Biol Cell. 2012. PMID: 22956764 Free PMC article.

2

Altered chondrocyte differentiation and extracellular matrix homeostasis in a zebrafish model for mucolipidosis II.

Flanagan-Steet H, Sias C, Steet R. Flanagan-Steet H, et al. Am J Pathol. 2009 Nov;175(5):2063-75. doi: 10.2353/ajpath.2009.090210. Epub 2009 Oct 15. Am J Pathol. 2009. PMID: 19834066 Free PMC article.

3

Selective yolk deposition and mannose phosphorylation of lysosomal glycosidases in zebrafish.

Fan X, Klein M, Flanagan-Steet HR, Steet R. Fan X, et al. J Biol Chem. 2010 Oct 22;285(43):32946-32953. doi: 10.1074/jbc.M110.158295. Epub 2010 Aug 20. J Biol Chem. 2010. PMID: 20729204 Free PMC article.

4

Mislocalization of large ARF-GEFs as a potential mechanism for BFA resistance in COG-deficient cells.

Flanagan-Steet H, Johnson S, Smith RD, Bangiyeva J, Lupashin V, Steet R. Flanagan-Steet H, et al. Exp Cell Res. 2011 Oct 1;317(16):2342-52. doi: 10.1016/j.yexcr.2011.06.005. Epub 2011 Jun 22. Exp Cell Res. 2011. PMID: 21722633 Free PMC article.

5

Excessive activity of cathepsin K is associated with cartilage defects in a zebrafish model of mucolipidosis II.

Petrey AC, Flanagan-Steet H, Johnson S, Fan X, De la Rosa M, Haskins ME, Nairn AV, Moremen KW, Steet R. Petrey AC, et al. Dis Model Mech. 2012 Mar;5(2):177-90. doi: 10.1242/dmm.008219. Epub 2011 Nov 1. Dis Model Mech. 2012. PMID: 22046029 Free PMC article.

6

Polar dibenzocyclooctynes for selective labeling of extracellular glycoconjugates of living cells.

Friscourt F, Ledin PA, Mbua NE, Flanagan-Steet HR, Wolfert MA, Steet R, Boons GJ. Friscourt F, et al. J Am Chem Soc. 2012 Mar 21;134(11):5381-9. doi: 10.1021/ja3002666. Epub 2012 Mar 9. J Am Chem Soc. 2012. PMID: 22376061 Free PMC article.

7

"Casting" light on the role of glycosylation during embryonic development: insights from zebrafish.

Flanagan-Steet HR, Steet R. Flanagan-Steet HR, et al. Glycoconj J. 2013 Jan;30(1):33-40. doi: 10.1007/s10719-012-9390-5. Epub 2012 May 26. Glycoconj J. 2013. PMID: 22638861 Free PMC article. Review.

8

The DMAP interaction domain of UDP-GlcNAc:lysosomal enzyme N-acetylglucosamine-1-phosphotransferase is a substrate recognition module.

Qian Y, Flanagan-Steet H, van Meel E, Steet R, Kornfeld SA. Qian Y, et al. Proc Natl Acad Sci U S A. 2013 Jun 18;110(25):10246-51. doi: 10.1073/pnas.1308453110. Epub 2013 Jun 3. Proc Natl Acad Sci U S A. 2013. PMID: 23733939 Free PMC article.

9

Abnormal accumulation and recycling of glycoproteins visualized in Niemann-Pick type C cells using the chemical reporter strategy.

Mbua NE, Flanagan-Steet H, Johnson S, Wolfert MA, Boons GJ, Steet R. Mbua NE, et al. Proc Natl Acad Sci U S A. 2013 Jun 18;110(25):10207-12. doi: 10.1073/pnas.1221105110. Epub 2013 Jun 3. Proc Natl Acad Sci U S A. 2013. PMID: 23733943 Free PMC article.

10

A mutation in a ganglioside biosynthetic enzyme, ST3GAL5, results in salt & pepper syndrome, a neurocutaneous disorder with altered glycolipid and glycoprotein glycosylation.

Boccuto L, Aoki K, Flanagan-Steet H, Chen CF, Fan X, Bartel F, Petukh M, Pittman A, Saul R, Chaubey A, Alexov E, Tiemeyer M, Steet R, Schwartz CE. Boccuto L, et al. Hum Mol Genet. 2014 Jan 15;23(2):418-33. doi: 10.1093/hmg/ddt434. Epub 2013 Sep 10. Hum Mol Genet. 2014. PMID: 24026681 Free PMC article.

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