Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation

Search Page

Filters

My Custom Filters

Publication date

Text availability

Article attribute

Article type

Additional filters

Article Language

Species

Sex

Age

Other

Search Results

56 results

Filters applied: . Clear all
Results are displayed in a computed author sort order. The Publication Date timeline is not available.
Page 1
Nonsense mutations accelerate lung disease and decrease survival of cystic fibrosis children.
Orenti A, Pranke I, Faucon C, Varilh J, Hatton A, Golec A, Dehillotte C, Durieu I, Reix P, Burgel PR, Grenet D, Tasset C, Gachelin E, Perisson C, Lepissier A, Dreano E, Tondelier D, Chevalier B, Weiss L, Kiefer S, Laurans M, Chiron R, Lemonnier L, Marguet C, Jung A, Edelman A, Kerem BS, Girodon E, Taulan-Cadars M, Hinzpeter A, Kerem E, Naehrlich L, Sermet-Gaudelus I; ECFSPR Steering group. Orenti A, et al. Among authors: tondelier d. J Cyst Fibros. 2023 Nov;22(6):1070-1079. doi: 10.1016/j.jcf.2023.06.005. Epub 2023 Jul 6. J Cyst Fibros. 2023. PMID: 37422433
An unexpected effect of TNF-α on F508del-CFTR maturation and function.
Bitam S, Pranke I, Hollenhorst M, Servel N, Moquereau C, Tondelier D, Hatton A, Urbach V, Sermet-Gaudelus I, Hinzpeter A, Edelman A. Bitam S, et al. Among authors: tondelier d. F1000Res. 2015 Jul 10;4:218. doi: 10.12688/f1000research.6683.2. eCollection 2015. F1000Res. 2015. PMID: 26594334 Free PMC article.
New insights into structure and function of bis-phosphinic acid derivatives and implications for CFTR modulation.
Bitam S, Elbahnsi A, Creste G, Pranke I, Chevalier B, Berhal F, Hoffmann B, Servel N, Baatalah N, Tondelier D, Hatton A, Moquereau C, Faria Da Cunha M, Pastor A, Lepissier A, Hinzpeter A, Mornon JP, Prestat G, Edelman A, Callebaut I, Gravier-Pelletier C, Sermet-Gaudelus I. Bitam S, et al. Among authors: tondelier d. Sci Rep. 2021 Mar 25;11(1):6842. doi: 10.1038/s41598-021-83240-x. Sci Rep. 2021. PMID: 33767236 Free PMC article.
Keratin 8 is a scaffolding and regulatory protein of ERAD complexes.
Pranke IM, Chevalier B, Premchandar A, Baatallah N, Tomaszewski KF, Bitam S, Tondelier D, Golec A, Stolk J, Lukacs GL, Hiemstra PS, Dadlez M, Lomas DA, Irving JA, Delaunay-Moisan A, van Anken E, Hinzpeter A, Sermet-Gaudelus I, Edelman A. Pranke IM, et al. Among authors: tondelier d. Cell Mol Life Sci. 2022 Sep;79(9):503. doi: 10.1007/s00018-022-04528-3. Epub 2022 Sep 1. Cell Mol Life Sci. 2022. PMID: 36045259
Factors influencing readthrough therapy for frequent cystic fibrosis premature termination codons.
Pranke I, Bidou L, Martin N, Blanchet S, Hatton A, Karri S, Cornu D, Costes B, Chevalier B, Tondelier D, Girodon E, Coupet M, Edelman A, Fanen P, Namy O, Sermet-Gaudelus I, Hinzpeter A. Pranke I, et al. Among authors: tondelier d. ERJ Open Res. 2018 Feb 23;4(1):00080-2017. doi: 10.1183/23120541.00080-2017. eCollection 2018 Jan. ERJ Open Res. 2018. PMID: 29497617 Free PMC article.
Characterization of two rat models of cystic fibrosis-KO and F508del CFTR-Generated by Crispr-Cas9.
Dreano E, Bacchetta M, Simonin J, Galmiche L, Usal C, Slimani L, Sadoine J, Tesson L, Anegon I, Concordet JP, Hatton A, Vignaud L, Tondelier D, Sermet-Gaudelus I, Chanson M, Cottart CH. Dreano E, et al. Among authors: tondelier d. Animal Model Exp Med. 2019 Nov 25;2(4):297-311. doi: 10.1002/ame2.12091. eCollection 2019 Dec. Animal Model Exp Med. 2019. PMID: 31942562 Free PMC article.
Effect of ouabain on CFTR gene expression in human Calu-3 cells.
Baudouin-Legros M, Brouillard F, Tondelier D, Hinzpeter A, Edelman A. Baudouin-Legros M, et al. Among authors: tondelier d. Am J Physiol Cell Physiol. 2003 Mar;284(3):C620-6. doi: 10.1152/ajpcell.00457.2002. Am J Physiol Cell Physiol. 2003. PMID: 12556359 Free article.
Author Correction: New insights into structure and function of bis-phosphinic acid derivatives and implications for CFTR modulation.
Bitam S, Elbahnsi A, Creste G, Pranke I, Chevalier B, Berhal F, Hoffmann B, Servel N, Baatalah N, Tondelier D, Hatton A, Moquereau C, Faria Da Cunha M, Pastor A, Lepissier A, Hinzpeter A, Mornon JP, Prestat G, Edelman A, Callebaut I, Gravier-Pelletier C, Sermet-Gaudelus I. Bitam S, et al. Among authors: tondelier d. Sci Rep. 2021 Sep 15;11(1):18709. doi: 10.1038/s41598-021-98301-4. Sci Rep. 2021. PMID: 34526640 Free PMC article. No abstract available.
56 results