Abstract
Recent studies have shown an up-regulation of the Fas/Fas ligand system in inflammatory myopathies. In myositis, however, the major Fas-mediated cytotoxicity which activates caspases bypasses apoptosis. We therefore evaluated the expression of proteins promoting cell survival, such as bcl-2, bcl-x(l) and cyclin-dependent kinase inhibitors, on muscle biopsies from 14 patients with polymyositis, dermatomyositis, inclusion body myositis and HIV-associated myositis. Our data demonstrate that inflammatory cells are immunoreactive for bcl-x(l), p16 and p57, three apoptosis-preventing proteins. Hence, we assume that these proteins might protect T cells from apoptotic nuclear changes. Our results could explain the non-self-limiting nature of inflammatory myopathies.
Publication types
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Research Support, Non-U.S. Gov't
MeSH terms
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Apoptosis / immunology*
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Biopsy
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CD3 Complex / analysis
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Cell Cycle Proteins*
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Cyclin-Dependent Kinase Inhibitor p16 / analysis
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Cyclin-Dependent Kinase Inhibitor p16 / immunology
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Cyclin-Dependent Kinase Inhibitor p21
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Cyclin-Dependent Kinase Inhibitor p27
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Cyclin-Dependent Kinase Inhibitor p57
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Cyclin-Dependent Kinases / antagonists & inhibitors
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Cyclins / analysis
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Cyclins / immunology
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Dermatomyositis / immunology
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Dermatomyositis / pathology
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Fas Ligand Protein
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HIV Infections / immunology
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HIV Infections / pathology
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Humans
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In Situ Nick-End Labeling
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Membrane Glycoproteins / analysis
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Membrane Glycoproteins / immunology
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Microtubule-Associated Proteins / analysis
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Microtubule-Associated Proteins / immunology
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Muscle, Skeletal / chemistry
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Muscle, Skeletal / immunology
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Muscle, Skeletal / pathology
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Myositis, Inclusion Body / immunology
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Myositis, Inclusion Body / pathology
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Nuclear Proteins / analysis
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Nuclear Proteins / immunology
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Polymyositis / immunology*
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Polymyositis / pathology*
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Proto-Oncogene Proteins c-bcl-2 / analysis
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Proto-Oncogene Proteins c-bcl-2 / immunology
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T-Lymphocytes / cytology*
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T-Lymphocytes / immunology*
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Tumor Suppressor Proteins*
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bcl-X Protein
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fas Receptor / analysis
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fas Receptor / immunology
Substances
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BCL2L1 protein, human
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CD3 Complex
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CDKN1A protein, human
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CDKN1C protein, human
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Cell Cycle Proteins
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Cyclin-Dependent Kinase Inhibitor p16
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Cyclin-Dependent Kinase Inhibitor p21
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Cyclin-Dependent Kinase Inhibitor p57
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Cyclins
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FASLG protein, human
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Fas Ligand Protein
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Membrane Glycoproteins
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Microtubule-Associated Proteins
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Nuclear Proteins
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Proto-Oncogene Proteins c-bcl-2
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Tumor Suppressor Proteins
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bcl-X Protein
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fas Receptor
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Cyclin-Dependent Kinase Inhibitor p27
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Cyclin-Dependent Kinases