Abstract
Resting energy expenditure (REE) was investigated in 8 children with propionic and methylmalonic acidaemias because a lowered REE has been reported in the literature. We observed a marginally elevated REE and think that adequate caloric intake and the use of a synthetic amino acid mixture are responsible for this.
MeSH terms
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Amino Acid Metabolism, Inborn Errors / drug therapy
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Amino Acid Metabolism, Inborn Errors / metabolism*
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Amino Acids / therapeutic use
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Child
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Child, Preschool
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Drug Combinations
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Energy Intake
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Energy Metabolism*
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Female
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Humans
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Infant
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Male
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Methylmalonic Acid / metabolism*
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Propionates / metabolism*
Substances
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Amino Acids
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Drug Combinations
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Propionates
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Methylmalonic Acid