TCR affinity and negative regulation limit autoimmunity

Nat Med. 2004 Nov;10(11):1234-9. doi: 10.1038/nm1114. Epub 2004 Oct 3.

Abstract

Autoimmune diseases are often mediated by self-reactive T cells, which must be activated to cause immunopathology. One mechanism, known as molecular mimicry, proposes that self-reactive T cells may be activated by pathogens expressing crossreactive ligands. Here we have developed a model to investigate how the affinity of the T-cell receptor (TCR) for the activating agent influences autoimmunity. Our model shows that an approximately fivefold difference in the TCR affinity for the activating ligand results in a 50% reduction in the incidence of autoimmunity. A reduction in TCR-ligand affinity to approximately 20 times lower than normal does not induce autoimmunity despite the unexpected induction of cytotoxic T lymphocytes (CTLs) and insulitis. Furthermore, in the absence of a key negative regulatory molecule, Cbl-b, 100% of mice develop autoimmunity upon infection with viruses encoding the lower-affinity ligand. Therefore, autoimmune disease is sensitive both to the affinity of the activating ligand and to normal mechanisms that negatively regulate the immune response.

Publication types

  • Comparative Study
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Animals
  • Autoimmunity / immunology*
  • Cell Proliferation
  • Chromium Radioisotopes
  • Diabetes Mellitus, Experimental / immunology
  • Flow Cytometry
  • Humans
  • Immunohistochemistry
  • Ligands
  • Lymphocytic choriomeningitis virus / immunology
  • Mice
  • Mice, Inbred C57BL
  • Mice, Transgenic
  • Models, Immunological*
  • Molecular Mimicry / immunology*
  • Receptors, Antigen, T-Cell / immunology*
  • Receptors, Antigen, T-Cell / metabolism*
  • T-Lymphocytes, Cytotoxic / immunology

Substances

  • Chromium Radioisotopes
  • Ligands
  • Receptors, Antigen, T-Cell