Cardiac-specific loss of N-cadherin leads to alteration in connexins with conduction slowing and arrhythmogenesis

Circ Res. 2005 Sep 2;97(5):474-81. doi: 10.1161/01.RES.0000181132.11393.18. Epub 2005 Aug 11.

Abstract

The remodeling of ventricular gap junctions, as defined by changes in size, distribution, or function, is a prominent feature of diseased myocardium. However, the regulation of assembly and maintenance of gap junctions remains poorly understood. To investigate N-cadherin function in the adult myocardium, we used a floxed N-cadherin gene in conjunction with a cardiac-specific tamoxifen-inducible Cre transgene. The mutant animals appeared active and healthy until their sudden death approximately 2 months after deleting N-cadherin from the heart. Electrophysiologic analysis revealed abnormal conduction in the ventricles of mutant animals, including diminished QRS complex amplitude consistent with loss of electrical coupling in the myocardium. A significant decrease in the gap junction proteins, connexin-43 and connexin-40, was observed in N-cadherin-depleted myocytes. Perturbation of connexin function resulted in decreased ventricular conduction velocity, as determined by optical mapping. Our data suggest that perturbation of the N-cadherin/catenin complex in heart disease may be an underlying cause, leading to the establishment of the arrythmogenic substrate by destabilizing gap junctions at the cell surface.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Animals
  • Arrhythmias, Cardiac / etiology*
  • Cadherins / physiology*
  • Connexin 43 / analysis*
  • Connexin 43 / physiology
  • Connexins / analysis*
  • Connexins / physiology
  • Death, Sudden, Cardiac / etiology
  • Electrocardiography
  • Gap Junction alpha-5 Protein
  • Gap Junctions / physiology
  • Mice
  • Mice, Knockout
  • Myocytes, Cardiac / chemistry*

Substances

  • Cadherins
  • Connexin 43
  • Connexins