Molecular pathogenesis of Hodgkin's lymphoma

J Clin Oncol. 2005 Sep 10;23(26):6379-86. doi: 10.1200/JCO.2005.55.013.

Abstract

According to the WHO classification, Hodgkin's lymphoma (HL) is subdivided into a classical variant and a nodular lymphocyte predominant variant which are characterized by the presence of Hodgkin's and Reed-Sternberg (H-RS) cells or lymphocytic and histiocytic (L&H) cells, respectively. This article reviews genetic characteristics and transcriptional changes of H-RS and L&H cells, including recent knowledge about transforming mechanisms and signaling pathways that contribute to the antiapoptotic phenotype displayed by H-RS and L&H cells. We also discuss major cellular and molecular mediators contributing to the establishment and maintenance of a reactive background in HL-affected tissues. We believe that an in-depth understanding of the pathogenesis of HL will eventually lead to the development of novel biologically based therapeutic strategies in the near future.

Publication types

  • Comparative Study
  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Female
  • Gene Expression Regulation, Neoplastic
  • Genetic Predisposition to Disease*
  • Hodgkin Disease / genetics*
  • Hodgkin Disease / physiopathology*
  • Humans
  • Male
  • Phenotype
  • Prognosis
  • Receptors, Cytokine / genetics
  • Receptors, Cytokine / metabolism
  • Receptors, Tumor Necrosis Factor / genetics
  • Receptors, Tumor Necrosis Factor / metabolism
  • Reed-Sternberg Cells / metabolism*
  • Sensitivity and Specificity
  • Severity of Illness Index

Substances

  • Receptors, Cytokine
  • Receptors, Tumor Necrosis Factor