Early preplasma cells define a tolerance checkpoint for autoreactive B cells

J Immunol. 2006 Jan 15;176(2):790-802. doi: 10.4049/jimmunol.176.2.790.

Abstract

Ab-secreting plasma cells (PCs) are the effectors of humoral immunity. In this study, we describe regulation of autoreactive B cells specific for the ribonucleoprotein Smith (Sm) at an early pre-PC stage. These cells are defined by the expression of the PC marker CD138 and normal levels of CD19 and B220. They are present at a high frequency in normal mouse spleen and bone marrow, are Ag dependent, and are located predominantly along the T cell-B cell border and near bridging channels. Anti-Sm pre-PCs also occur at a high frequency in nonautoimmune mice and show additional phenotypic characteristics of PC differentiation. However, while some of these pre-PCs are Ab-secreting cells, those specific for Sm are not, indicating regulation. Consistent with this, anti-Sm pre-PCs have a higher turnover rate and higher frequency of cell death than those that do not bind Sm. Regulation of anti-Sm pre-PCs occurs upstream of the transcriptional repressor, B lymphocyte-induced maturation protein-1, expression. Regulation at this stage is overcome in autoimmune MRL/lpr mice and is accompanied by an altered B lymphocyte stimulator receptor profile. These data reveal a new B cell tolerance checkpoint that is overcome in autoimmunity.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Animals
  • Apoptosis / immunology
  • Autoantigens
  • Autoimmunity / genetics
  • B-Lymphocytes / cytology
  • B-Lymphocytes / immunology*
  • Base Sequence
  • Cell Differentiation
  • DNA / genetics
  • Immune Tolerance* / genetics
  • Membrane Glycoproteins / metabolism
  • Mice
  • Mice, Inbred MRL lpr
  • Mice, Transgenic
  • Plasma Cells / cytology
  • Plasma Cells / immunology*
  • Positive Regulatory Domain I-Binding Factor 1
  • Proteoglycans / metabolism
  • Receptors, Tumor Necrosis Factor / genetics
  • Repressor Proteins / genetics
  • Ribonucleoproteins, Small Nuclear / immunology
  • Spleen / cytology
  • Spleen / immunology
  • Syndecan-1
  • Syndecans
  • Transcription Factors / genetics
  • Transcription, Genetic
  • snRNP Core Proteins

Substances

  • Autoantigens
  • BLyS receptor
  • Membrane Glycoproteins
  • Prdm1 protein, mouse
  • Proteoglycans
  • Receptors, Tumor Necrosis Factor
  • Repressor Proteins
  • Ribonucleoproteins, Small Nuclear
  • SDC1 protein, human
  • Sdc1 protein, mouse
  • Syndecan-1
  • Syndecans
  • Transcription Factors
  • snRNP Core Proteins
  • DNA
  • Positive Regulatory Domain I-Binding Factor 1