Complex chromosome 8;21 translocation with associated hyperdiploidy in acute myeloid leukemia (FAB-M2)

Pediatr Blood Cancer. 2008 Mar;50(3):651-4. doi: 10.1002/pbc.21192.

Abstract

We present a case of acute myeloblastic leukemia (AML-M2) with a complex t(8;21) translocation and additional acquired chromosomes yielding a hyperdiploid karyotype. AML1/ETO transcript was observed by reverse transcription-polymerase chain reaction. Fluorescence in situ hybridization (FISH), spectral karyotyping (SKY), and comparative genomic hybridization (CGH) were performed to further identify the chromosomes observed by G banding. The patient was treated according to our current protocol for AML. He remains in complete remission +11 months from diagnosis. Further follow-up of this patient and the analysis of a larger number of children are needed to define whether the gains of the specific extra chromosomes modify the good prognosis that t(8;21) confers to this subgroup of AML.

Publication types

  • Case Reports
  • Comparative Study

MeSH terms

  • Aneuploidy*
  • Antineoplastic Combined Chemotherapy Protocols / administration & dosage
  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use
  • Child
  • Chromosomes, Human, Pair 21 / genetics
  • Chromosomes, Human, Pair 21 / ultrastructure*
  • Chromosomes, Human, Pair 8 / genetics
  • Chromosomes, Human, Pair 8 / ultrastructure*
  • Core Binding Factor Alpha 2 Subunit / genetics*
  • Cytarabine / administration & dosage
  • Cytogenetic Analysis
  • Etoposide / administration & dosage
  • Humans
  • Idarubicin / administration & dosage
  • Leukemia, Myeloid, Acute / drug therapy
  • Leukemia, Myeloid, Acute / genetics*
  • Male
  • Nucleic Acid Hybridization
  • Oncogene Proteins, Fusion / genetics*
  • Polymerase Chain Reaction
  • RUNX1 Translocation Partner 1 Protein
  • Translocation, Genetic*

Substances

  • AML1-ETO fusion protein, human
  • Core Binding Factor Alpha 2 Subunit
  • Oncogene Proteins, Fusion
  • RUNX1 Translocation Partner 1 Protein
  • Cytarabine
  • Etoposide
  • Idarubicin

Supplementary concepts

  • ICE protocol 4