Basement membrane derived fibulin-1 and fibulin-5 function as angiogenesis inhibitors and suppress tumor growth

Exp Biol Med (Maywood). 2008 Feb;233(2):155-62. doi: 10.3181/0706-RM-167.

Abstract

The fibulins are a family of secreted glycoproteins that are characterized by repeated epidermal-growth-factor-like domains and a unique C-terminus structure. Fibulins modulate cell morphology, growth, adhesion, and motility. Our initial basement membrane degradome screen using Cathepsin D, a tumor microenvironment-associated protease, contained fragments of fibulin-1 and full length fibulin-5. In this report, we evaluate the antiangiogenic activity of fibulin-1 and fibulin-5. Tumor studies demonstrate that both fibulin-1 and fibulin-5 suppress HT1080 tumor growth. CD31 labeling and TUNEL assay further reveal that fibulin-1 suppression of HT1080 tumor growth is associated with diminished angiogenesis and also enhanced apoptosis of endothelial cells and tumor cells. In contrast, fibulin-5 inhibits tumor angiogenesis with a minimal anti-apoptotic affect. Cathepsin D digestion of fibulin-1 produces a fragment with nearly the same molecular weight as fibulin-5, and this fragment (named Neostatin) inhibits endothelial cell proliferation. Additionally, degradation of basement membrane by cathepsin D liberates both fibulin-1 fragments and fibulin-5, which function to inhibit angiogenesis.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Sequence
  • Angiogenesis Inhibitors / genetics
  • Angiogenesis Inhibitors / isolation & purification
  • Angiogenesis Inhibitors / metabolism
  • Angiogenesis Inhibitors / pharmacology*
  • Animals
  • Basement Membrane / metabolism*
  • Calcium-Binding Proteins / genetics
  • Calcium-Binding Proteins / isolation & purification
  • Calcium-Binding Proteins / metabolism
  • Calcium-Binding Proteins / pharmacology*
  • Cathepsin D / metabolism
  • Cattle
  • Cell Proliferation / drug effects
  • Cloning, Molecular
  • Conserved Sequence
  • Endothelial Cells / cytology
  • Endothelial Cells / drug effects
  • Extracellular Matrix Proteins / genetics
  • Extracellular Matrix Proteins / isolation & purification
  • Extracellular Matrix Proteins / metabolism
  • Extracellular Matrix Proteins / pharmacology*
  • Humans
  • Molecular Sequence Data
  • Molecular Weight
  • Neoplasms / pathology*
  • Recombinant Proteins / genetics
  • Recombinant Proteins / isolation & purification
  • Recombinant Proteins / metabolism
  • Recombinant Proteins / pharmacology
  • Sequence Alignment

Substances

  • Angiogenesis Inhibitors
  • Calcium-Binding Proteins
  • Extracellular Matrix Proteins
  • FBLN5 protein, human
  • Recombinant Proteins
  • fibulin
  • Cathepsin D