Preservation of long-term memory and synaptic plasticity despite short-term impairments in the Tc1 mouse model of Down syndrome

Learn Mem. 2008 Jul 14;15(7):492-500. doi: 10.1101/lm.969608. Print 2008 Jul.

Abstract

Down syndrome (DS) is a genetic disorder arising from the presence of a third copy of the human chromosome 21 (Hsa21). Recently, O'Doherty and colleagues in an earlier study generated a new genetic mouse model of DS (Tc1) that carries an almost complete Hsa21. Since DS is the most common genetic cause of mental retardation, we have undertaken a detailed analysis of cognitive function and synaptic plasticity in Tc1 mice. Here we show that Tc1 mice have impaired spatial working memory (WM) but spared long-term spatial reference memory (RM) in the Morris watermaze. Similarly, Tc1 mice are selectively impaired in short-term memory (STM) but have intact long-term memory (LTM) in the novel object recognition task. The pattern of impaired STM and normal LTM is paralleled by a corresponding phenotype in long-term potentiation (LTP). Freely-moving Tc1 mice exhibit reduced LTP 1 h after induction but normal maintenance over days in the dentate gyrus of the hippocampal formation. Biochemical analysis revealed a reduction in membrane surface expression of the AMPAR (alpha-amino-3-hydroxy-5-methyl-4-propionic acid receptor) subunit GluR1 in the hippocampus of Tc1 mice, suggesting a potential mechanism for the impairment in early LTP. Our observations also provide further evidence that STM and LTM for hippocampus-dependent tasks are subserved by parallel processing streams.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Analysis of Variance
  • Animals
  • Chromosomes, Human, Pair 21
  • Discrimination Learning / physiology
  • Disease Models, Animal
  • Down Syndrome* / genetics
  • Down Syndrome* / pathology
  • Down Syndrome* / physiopathology
  • Electrophysiology
  • Exploratory Behavior / physiology
  • Hippocampus / physiopathology
  • Hippocampus / radiation effects
  • Humans
  • In Vitro Techniques
  • Long-Term Potentiation / genetics
  • Long-Term Potentiation / physiology
  • Maze Learning / physiology
  • Memory Disorders / genetics
  • Memory Disorders / physiopathology*
  • Memory, Short-Term / physiology*
  • Mice
  • Mice, Inbred C57BL
  • Mice, Mutant Strains
  • Neuronal Plasticity / physiology*
  • Pattern Recognition, Physiological / physiology
  • Receptors, AMPA / genetics
  • Receptors, AMPA / metabolism
  • Spatial Behavior / physiology
  • Trisomy

Substances

  • Receptors, AMPA
  • glutamate receptor ionotropic, AMPA 1