The regulation of autoreactive B cells during innate immune responses

Immunol Res. 2008;41(3):295-309. doi: 10.1007/s12026-008-8039-8.

Abstract

Systemic lupus erythematosus (SLE) highlights the dangers of dysregulated B cells and the importance of initiating and maintaining tolerance. In addition to central deletion, receptor editing, peripheral deletion, receptor revision, anergy, and indifference, we have described a new mechanism of B cell tolerance wherein dendritic cells (DCs) and macrophages (MPhis) regulate autoreactive B cells during innate immune responses. In part, DCs and MPhis repress autoreactive B cells by releasing IL-6 and soluble CD40L (sCD40L). This mechanism is selective in that IL-6 and sCD40L do not affect Ig secretion by naïve cells during innate immune responses, allowing immunity in the absence of autoimmunity. In lupus-prone mice, DCs and MPhis are defective in secretion of IL-6 and sCD40L and cannot effectively repress autoantibody secretion suggesting that defects in DC/MPhi-mediated tolerance may contribute to the autoimmune phenotype. Further, these studies suggest that reconstituting DCs and MPhis in SLE patients might restore regulation of autoreactive B cells and provide an alternative to immunosuppressive therapies.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Autoantibodies / immunology
  • Autoantibodies / metabolism
  • Autoantigens / immunology
  • Autoantigens / metabolism
  • Autoimmunity / immunology
  • B-Lymphocytes / immunology*
  • B-Lymphocytes / metabolism
  • CD40 Ligand / immunology
  • CD40 Ligand / metabolism
  • Dendritic Cells / immunology*
  • Dendritic Cells / metabolism
  • Humans
  • Immune Tolerance / immunology*
  • Interleukin-6 / immunology
  • Interleukin-6 / metabolism
  • Lupus Erythematosus, Systemic / immunology*
  • Lupus Erythematosus, Systemic / metabolism
  • Macrophages / immunology*
  • Macrophages / metabolism
  • snRNP Core Proteins / immunology
  • snRNP Core Proteins / metabolism

Substances

  • Autoantibodies
  • Autoantigens
  • Interleukin-6
  • snRNP Core Proteins
  • CD40 Ligand