Abstract
An infant initially diagnosed with a parotid hemangioma presented with stridor and thrombocytopenia. Diagnosis of Kaposiform hemangioendothelioma was confirmed with biopsy. The child succumbed to multi-system organ failure related to consumptive coagulopathy despite aggressive medical management. Kaposiform hemangioendothelioma is a rare head and neck tumor that may be mistaken for a hemangioma on preliminary diagnosis, which may lead to increased morbidity and mortality especially in the setting of Kasabach-Merritt phenomenon. A platelet count may provide an early and important clue to the possibility of coagulopathy; prompting physicians to look for a diagnosis other than a simple hemangioma.
MeSH terms
-
Antineoplastic Combined Chemotherapy Protocols / therapeutic use
-
Disease Progression
-
Disseminated Intravascular Coagulation / diagnosis
-
Disseminated Intravascular Coagulation / therapy
-
Fatal Outcome
-
Female
-
Hemangioendothelioma / diagnosis
-
Hemangioendothelioma / therapy
-
Hemangioma, Capillary / diagnosis
-
Hemangioma, Capillary / therapy
-
Hemangioma, Cavernous / diagnosis
-
Hemangioma, Cavernous / therapy
-
Humans
-
Infant, Newborn
-
Kasabach-Merritt Syndrome
-
Laryngeal Neoplasms / diagnosis*
-
Laryngeal Neoplasms / therapy
-
Laryngoscopy / methods
-
Magnetic Resonance Imaging / methods
-
Multiple Organ Failure / diagnosis*
-
Multiple Organ Failure / etiology
-
Risk Assessment
-
Sarcoma, Kaposi / diagnosis
-
Sarcoma, Kaposi / therapy
-
Severity of Illness Index
-
Skin Neoplasms / diagnosis
-
Skin Neoplasms / therapy
-
Thrombocytopenia / diagnosis
-
Thrombocytopenia / therapy
-
Tracheostomy / methods
-
Vascular Neoplasms / diagnosis
-
Vascular Neoplasms / therapy
Supplementary concepts
-
Kaposiform Hemangioendothelioma