Intraosseous arteriovenous maxillomandibular malformations are rare. The diagnosis is primarily clinical (children with pulsatile osseous tumefaction, bleeding at cingulum), completed with imaging techniques (TDM and/or MRI). Arteriography is indicated only at the time of therapeutic management. The evolution may vary greatly (four levels: quiescence, expansion, destruction, decompensation) and usually evolves because of hormonal changes or trauma. Radiotherapy and vascular ligatures are no longer recommended. The best treatment is direct or transarterial embolization. Surgical resection, when feasible, must be thorough. It is indicated in case of failure or recurrence after embolization.