Some novel features of IDH1-mutated acute myeloid leukemia revealed in Chinese patients

Leuk Res. 2011 Oct;35(10):1301-6. doi: 10.1016/j.leukres.2011.01.019. Epub 2011 Feb 12.

Abstract

Mutations of isocitrate dehydrogenase 1 (IDH1) have recently been reported in acute myeloid leukemia (AML). However, the characteristics of IDH1-mutated AML are still not known clearly. We analyzed 416 Chinese AML patients and found 28 patients (6.7%) carried this mutation. One homozygous IDH1 mutant in AML was found. The IDH1 mutations were associated with NPM1 mutations (P=0.043) and could coexist with recurrent transcription factor aberrations including AML1-ETO (6/50), PML-RARα (3/77) and CBFβ-MYH11 (1/15). For AML with AML1-ETO fusion gene, IDH1(mut) patients may have worse disease-free survival (DFS) than IDH1(wild-type) patients.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Asian People / genetics*
  • Core Binding Factor Alpha 2 Subunit / genetics*
  • Disease-Free Survival
  • Female
  • Genetic Linkage
  • Genotype
  • Heterozygote
  • Homozygote
  • Humans
  • Isocitrate Dehydrogenase / genetics*
  • Karyotyping
  • Leukemia, Myeloid, Acute / diagnosis
  • Leukemia, Myeloid, Acute / genetics*
  • Leukemia, Myeloid, Acute / mortality
  • Leukemia, Myeloid, Acute / pathology
  • Male
  • Middle Aged
  • Mutation
  • Nuclear Proteins / genetics
  • Nucleophosmin
  • Oncogene Proteins, Fusion / genetics*
  • Polymerase Chain Reaction
  • Prognosis
  • RUNX1 Translocation Partner 1 Protein
  • Recurrence
  • Restriction Mapping

Substances

  • AML1-ETO fusion protein, human
  • CBFbeta-MYH11 fusion protein
  • Core Binding Factor Alpha 2 Subunit
  • NPM1 protein, human
  • Nuclear Proteins
  • Oncogene Proteins, Fusion
  • RUNX1 Translocation Partner 1 Protein
  • promyelocytic leukemia-retinoic acid receptor alpha fusion oncoprotein
  • Nucleophosmin
  • Isocitrate Dehydrogenase