We report the case of a 75-year-old woman who presented the association of a cecal volvulus with an appendiceal mucocele. A laparotomy showed these two findings and a right hemicolectomy with an end-to-end ileo-transverse colonic anastomosis was done. The role of plain radiograph and computerized tomographic imaging in the diagnosis of this entity is discussed To our knowledge, this association has not been reported in the literature.