Anti-neuronal and stress-induced-phosphoprotein 1 antibodies in neuro-Behçet's disease

J Neuroimmunol. 2011 Oct 28;239(1-2):91-7. doi: 10.1016/j.jneuroim.2011.08.008. Epub 2011 Aug 27.

Abstract

No disease-specific neuronal antibodies have so far been defined in neuro-Behçet's disease (NBD). Immunohistochemistry and immunocytochemistry studies showed antibodies to hippocampal and cerebellar molecular layers and the surface antigens of cultured hippocampal neurons in sera and/or cerebrospinal fluids (CSF) of 13 of 20 NBD and 6 of 20 BD patients but not in multiple sclerosis or headache controls. Screening with a protein macroarray led to identification of stress-induced-phosphoprotein-1 (STIP-1) as an antigenic target. High-titer STIP-1-antibodies were detected in 6 NBD patients' sera but not in controls. These results suggest that neuronal antibodies could be useful as diagnostic biomarkers in NBD.

Publication types

  • Comparative Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Animals
  • Autoantibodies / biosynthesis*
  • Behcet Syndrome / immunology*
  • Behcet Syndrome / metabolism
  • Behcet Syndrome / pathology
  • Female
  • Heat-Shock Proteins / blood
  • Heat-Shock Proteins / immunology*
  • Hippocampus / blood supply
  • Hippocampus / immunology
  • Hippocampus / pathology
  • Humans
  • Male
  • Mannose-Binding Protein-Associated Serine Proteases / physiology
  • Middle Aged
  • Multiple Sclerosis / immunology
  • Multiple Sclerosis / metabolism
  • Multiple Sclerosis / pathology
  • Nerve Degeneration / immunology*
  • Nerve Degeneration / metabolism
  • Nerve Degeneration / pathology
  • Neurons / immunology*
  • Neurons / metabolism
  • Neurons / pathology
  • Organ Specificity / immunology
  • Rats

Substances

  • Autoantibodies
  • Heat-Shock Proteins
  • STIP1 protein, human
  • MASP2 protein, human
  • Mannose-Binding Protein-Associated Serine Proteases