Inverse Gottron's papules: an unusual cutaneous manifestation of juvenile dermatomyositis

Pediatr Dermatol. 2012 Sep-Oct;29(5):641-4. doi: 10.1111/j.1525-1470.2011.01585.x. Epub 2011 Dec 30.

Abstract

Dermatomyositis is an autoimmune inflammatory myopathy characterized by unique cutaneous features. Gottron's papules are pathognomonic, lichenoid papules that can be found overlying the joints of the dorsal hand. Papules on the palms of the hand are less commonly seen, especially in the pediatric age group. Recognition of these inverse Gottron's papules as a sign of dermatomyositis is important as they may be the only cutaneous feature and may be a clue of underlying interstitial lung disease.

Publication types

  • Case Reports

MeSH terms

  • Adrenal Cortex Hormones
  • Androstadienes / therapeutic use
  • Child
  • Child, Preschool
  • Dermatomyositis / drug therapy
  • Dermatomyositis / pathology*
  • Female
  • Fluticasone
  • Humans
  • Immunoglobulins, Intravenous / therapeutic use
  • Immunosuppressive Agents / therapeutic use
  • Lung Diseases, Interstitial / diagnosis
  • Lung Diseases, Interstitial / drug therapy
  • Male
  • Methotrexate / therapeutic use
  • Mycophenolic Acid / analogs & derivatives
  • Mycophenolic Acid / therapeutic use
  • Prednisone / therapeutic use
  • Treatment Outcome

Substances

  • Adrenal Cortex Hormones
  • Androstadienes
  • Immunoglobulins, Intravenous
  • Immunosuppressive Agents
  • Fluticasone
  • Mycophenolic Acid
  • Prednisone
  • Methotrexate

Supplementary concepts

  • Amyopathic dermatomyositis