Anti-leukemic mechanisms of pegylated arginase I in acute lymphoblastic T-cell leukemia

Leukemia. 2013 Mar;27(3):569-77. doi: 10.1038/leu.2012.247. Epub 2012 Aug 28.

Abstract

New treatments for adults with acute lymphoblastic T-cell leukemia (T-ALL) are urgently needed, as the current rate of overall remission in these patients is only about 40 percent. We recently showed the potential therapeutic benefit of the pegylated-human-arginase I (peg-Arg I) in T-ALL. However, the mechanisms by which peg-Arg I induces an anti-T-ALL effect remained unknown. Our results show the induction of T-ALL cell apoptosis by peg-Arg I, which associated with a global arrest in protein synthesis and with the phosphorylation of the eukaryotic-translation-initiation factor 2 alpha (eIF2α). Inhibition of eIF2α phosphorylation in T-ALL cells prevented the apoptosis induced by peg-Arg I, whereas the expression of a phosphomimetic eIF2α form increased the sensibility of T-ALL cells to peg-Arg I. Phosphorylation of eIF2α by peg-Arg I was mediated through kinases PERK and GCN2 and down-regulation of phosphatase GADD34. GCN2 and decreased GADD34 promoted T-ALL cell apoptosis after treatment with peg-Arg I, whereas PERK had an unexpected anti-apoptotic role. Additional results showed that phospho-eIF2α signaling further increased the anti-leukemic effects induced by peg-Arg I in T-ALL-bearing mice. These results suggest the central role of phospho-eIF2α in the anti-T-ALL effects induced by peg-Arg I and support its study as a therapeutic target.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Animals
  • Apoptosis / drug effects
  • Arginase / administration & dosage*
  • Blotting, Western
  • Cell Proliferation / drug effects
  • Eukaryotic Initiation Factor-2 / metabolism*
  • Female
  • Fluorescent Antibody Technique
  • Humans
  • Mice
  • Mice, Inbred NOD
  • Mice, SCID
  • Phosphorylation
  • Polyethylene Glycols / chemistry*
  • Precursor T-Cell Lymphoblastic Leukemia-Lymphoma / metabolism
  • Precursor T-Cell Lymphoblastic Leukemia-Lymphoma / pathology
  • Precursor T-Cell Lymphoblastic Leukemia-Lymphoma / prevention & control*
  • Protein Phosphatase 1 / metabolism*
  • Protein Serine-Threonine Kinases / metabolism*
  • Recombinant Proteins / therapeutic use
  • Signal Transduction
  • Survival Rate
  • eIF-2 Kinase / metabolism*

Substances

  • Eukaryotic Initiation Factor-2
  • Recombinant Proteins
  • Polyethylene Glycols
  • EIF2AK4 protein, human
  • PERK kinase
  • Protein Serine-Threonine Kinases
  • eIF-2 Kinase
  • PPP1R15A protein, human
  • Protein Phosphatase 1
  • Arginase