GABAB receptor antibodies in paraneoplastic cerebellar ataxia

J Neuroimmunol. 2013 Mar 15;256(1-2):94-6. doi: 10.1016/j.jneuroim.2012.12.006. Epub 2013 Jan 14.

Abstract

Autoantibodies to the gamma-aminobutyric acid-B (GABAB) receptor were recently described in patients with limbic encephalitis presenting with early or prominent seizures. We report on a 64-year-old man with malignant melanoma who during adjuvant therapy with interferon (IFN)-alpha developed cerebellar ataxia. Indirect immunofluorescence on brain tissue sections revealed high-titer (1:20,000) IgG1 serum autoantibodies to the cerebellar molecular and granular layer, which were confirmed to be directed against GABAB receptor in a cell-based assay. This case highlights cerebellar ataxia in the absence of seizures as a clinical manifestation of GABAB receptor autoimmunity and extends the spectrum of tumors underlying this condition to malignant melanoma. IFN-alpha therapy may have contributed to the development of autoimmunity in this patient.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Antibodies / metabolism*
  • Brain / metabolism*
  • Cell Line, Transformed
  • Cerebellar Ataxia / chemically induced
  • Cerebellar Ataxia / pathology*
  • Humans
  • Immunologic Factors / adverse effects
  • Interferon-alpha / adverse effects
  • Male
  • Melanoma / drug therapy
  • Middle Aged
  • Receptors, GABA-B / immunology*

Substances

  • Antibodies
  • Immunologic Factors
  • Interferon-alpha
  • Receptors, GABA-B