Assessing exertional dyspnea in patients with idiopathic pulmonary fibrosis

Respir Med. 2014 Jan;108(1):181-8. doi: 10.1016/j.rmed.2013.12.009. Epub 2013 Dec 24.

Abstract

Background: Dyspnea is a hallmark symptom of idiopathic pulmonary fibrosis (IPF), and dyspnea induced physical activity limitation is a prominent driver of quality of life impairment among IPF patients.

Methods: We examined response data for the 21 physical activity items (the first 21 of 24) from the University of California San Diego Shortness of Breath Questionnaire (UCSD) collected at baseline in a recently conducted IPF trial. We used Rasch analysis and hypothesis testing with conventional statistical methodology to achieve three objectives: 1) to examine the items to identify the one characteristic that distinguishes one from another; 2) to asses these items for their ability to measure dyspnea severity in IPF; 3) to use the items to develop a dyspnea ruler.

Results: The sample comprised 178 subjects. The 21 items fit the Rasch model. There was very strong correlation between Rasch item severity and their metabolic equivalents (METS) values (r = -0.86, p < 0.0001). With the sample stratified on scores from the 21 items, there were significant between group differences in FVC%, DLCO% and distance walked during the six-minute walk test. The dyspnea ruler can be used to put dyspnea levels in a more easily understood clinical context.

Conclusions: The first 21 items from the UCSD compose a unidimensional dyspnea-with-activity scale and are both sensibly ordered and distinguished from each other by their METS values. These 21 items can be used confidently to formulate clinically-relevant inferences about IPF patients and should be considered for use as a meaningful endpoint in IPF research.

Keywords: Dyspnea; Functional capacity; Idiopathic pulmonary fibrosis; Quality of life.

Publication types

  • Research Support, N.I.H., Extramural
  • Validation Study

MeSH terms

  • Aged
  • Controlled Clinical Trials as Topic
  • Dyspnea / drug therapy
  • Dyspnea / etiology
  • Dyspnea / physiopathology*
  • Exercise Test*
  • Female
  • Humans
  • Idiopathic Pulmonary Fibrosis / complications
  • Idiopathic Pulmonary Fibrosis / physiopathology*
  • Male
  • Middle Aged
  • Piperazines / therapeutic use
  • Purines / therapeutic use
  • Quality of Life*
  • Reproducibility of Results
  • Research Design*
  • Severity of Illness Index
  • Sildenafil Citrate
  • Sulfones / therapeutic use
  • Surveys and Questionnaires / standards*
  • Vasodilator Agents / therapeutic use
  • Walking*

Substances

  • Piperazines
  • Purines
  • Sulfones
  • Vasodilator Agents
  • Sildenafil Citrate