Aberrant activation of the WNT/β-catenin signaling pathway in lupus nephritis

PLoS One. 2014 Jan 21;9(1):e84852. doi: 10.1371/journal.pone.0084852. eCollection 2014.

Abstract

Objective: The canonical WNT pathway has been implicated as playing important roles in the pathogenesis of a variety of kidney diseases. Recently, WNT pathway activity was reported to be elevated in the renal tissue of a lupus mouse model. This study aimed to evaluate the potential role of the WNT pathway in the pathogenesis of human lupus nephritis.

Methods: The expression of β-catenin was evaluated in renal biopsy specimens from lupus nephritis patients and control kidney tissues by immunohistochemistry and western blotting. Real-time polymerase chain reaction (RT-PCR) was used to detect RNA expression of β-catenin, Dkk-1 and Axin2. Plasma concentrations of Dkk-1 were measured by ELISA.

Results: Immunohistochemistry and western blotting revealed increased expression of β-catenin in the kidneys of patients with lupus nephritis compared with control kidney tissues (p<0.05), accompanied by an increase in mRNA expression of β-catenin (p<0.01) and axin2 (p<0.05). β-catenin was significantly greater in LN patients without renal interstitial fibrosis compared with those with renal interstitial fibrosis (p<0.01) at the mRNA expression level; the increase in β-catenin mRNA positively correlated with the creatinine clearance rate (Ccr) and negatively correlated with chronicity indices of renal tissue injury. Greater plasma Dkk-1 concentrations were found in LN patients compared with controls (p<0.05). Plasma Dkk-1 concentrations also correlated negatively with anti-dsDNA antibody levels and positively with serum C3 levels.

Conclusions: The canonical WNT/β-catenin signaling pathway was activated in lupus nephritis patients, accompanied by an increase in plasma levels of Dkk-1. Altered WNT/β-catenin signaling was related to the pathogenesis of lupus nephritis and might play a role in renal fibrosis.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Antibodies, Antinuclear / blood
  • Axin Protein / genetics
  • Axin Protein / metabolism
  • Case-Control Studies
  • Complement C3 / metabolism
  • Creatinine / blood
  • Female
  • Fibrosis
  • Gene Expression
  • Humans
  • Intercellular Signaling Peptides and Proteins / blood
  • Intercellular Signaling Peptides and Proteins / genetics
  • Kidney / metabolism
  • Kidney / pathology
  • Kidney Function Tests
  • Lupus Nephritis / genetics*
  • Lupus Nephritis / metabolism
  • Lupus Nephritis / pathology*
  • Male
  • Middle Aged
  • RNA, Messenger / genetics*
  • RNA, Messenger / metabolism
  • Wnt Signaling Pathway / genetics*
  • beta Catenin / genetics
  • beta Catenin / metabolism

Substances

  • AXIN2 protein, human
  • Antibodies, Antinuclear
  • Axin Protein
  • CTNNB1 protein, human
  • Complement C3
  • DKK1 protein, human
  • Intercellular Signaling Peptides and Proteins
  • RNA, Messenger
  • beta Catenin
  • Creatinine

Grants and funding

This work was supported in part by the Special Fund for Public Benefit Research from Ministry of Health (201202004), the National Natural Science Foundation of China (No. 30801026), the Doctoral Innovation Fund of Shanghai Jiao Tong University School of Medicine (BXJ201020). The funders had no role in study design, data collection and analysis, decision to publish, or preparation of the manuscript.