Molecular basis for disruption of E-cadherin adhesion by botulinum neurotoxin A complex

Science. 2014 Jun 20;344(6190):1405-10. doi: 10.1126/science.1253823.

Abstract

How botulinum neurotoxins (BoNTs) cross the host intestinal epithelial barrier in foodborne botulism is poorly understood. Here, we present the crystal structure of a clostridial hemagglutinin (HA) complex of serotype BoNT/A bound to the cell adhesion protein E-cadherin at 2.4 angstroms. The HA complex recognizes E-cadherin with high specificity involving extensive intermolecular interactions and also binds to carbohydrates on the cell surface. Binding of the HA complex sequesters E-cadherin in the monomeric state, compromising the E-cadherin-mediated intercellular barrier and facilitating paracellular absorption of BoNT/A. We reconstituted the complete 14-subunit BoNT/A complex using recombinantly produced components and demonstrated that abolishing either E-cadherin- or carbohydrate-binding of the HA complex drastically reduces oral toxicity of BoNT/A complex in vivo. Together, these studies establish the molecular mechanism of how HAs contribute to the oral toxicity of BoNT/A.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, Non-P.H.S.

MeSH terms

  • Animals
  • Botulinum Toxins, Type A / chemistry*
  • Botulinum Toxins, Type A / genetics
  • Cadherins / chemistry*
  • Cadherins / genetics
  • Crystallography, X-Ray
  • Gene Knockdown Techniques
  • HT29 Cells
  • Hemagglutinins / chemistry*
  • Hemagglutinins / genetics
  • Humans
  • Mice
  • Protein Structure, Secondary
  • Recombinant Proteins / chemistry

Substances

  • Cadherins
  • Hemagglutinins
  • Recombinant Proteins
  • Botulinum Toxins, Type A

Associated data

  • PDB/4QD2