Newborn screening for congenital hypothyroidism, galactosemia and biotinidase deficiency in Uttar Pradesh, India

Indian Pediatr. 2014 Sep;51(9):701-5. doi: 10.1007/s13312-014-0485-x.

Abstract

Objective: To assess feasibility and recall rates for newborn screening for congenital hypothyroidism, galactosemia and biotinidase deficiency in a predominantly rural and inner city population in and around the City of Lucknow in Uttar Pradesh, India.

Design: Prospective observational study.

Setting: Two tertiary-care and 5 district hospitals in and around Lucknow.

Participants: All babies born in above hospitals during the study period.

Methods: Heel prick samples were collected after 24 hours of life. Dried blood spot TSH, total galactose and biotinidase were assayed by immunofluorometry. Age related cut-offs were applied for recall for TSH. For galactosemia and biotinidase deficiency, manufacturer-suggested recall cut-offs used initially were modified after analysis of initial data.

Main outcome measure: Recall rate for hypothyroidism, galactosemia and biotinidase deficiency.

Results: Screening was carried out for 13426 newborns, 73% of all deliveries. Eighty-five percent of those recalled for confirmatory sampling responded. Using fixed TSH cut off of 20 mIU/L yielded high recall rate of 1.39%, which decreased to 0.84% with use of age-related cut-offs. Mean TSH was higher in males, and in low birth weight and vaginally delivered babies. Eleven babies had congenital hypothyroidism. Recall rates with modified cut-offs for galactosemia and biotinidase deficiency were 0.32% and 0.16%, respectively.

Conclusions: An outreach program for newborn screening can be successfully carried out in similar socio-cultural settings in India. For hypothyroidism, the high recall rate due to early discharge was addressed by age-related cut-offs.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Biotinidase Deficiency / diagnosis*
  • Biotinidase Deficiency / epidemiology
  • Congenital Hypothyroidism / diagnosis*
  • Congenital Hypothyroidism / epidemiology
  • Dried Blood Spot Testing
  • Female
  • Galactosemias / diagnosis*
  • Galactosemias / epidemiology
  • Humans
  • India / epidemiology
  • Infant, Newborn
  • Male
  • Neonatal Screening* / methods
  • Neonatal Screening* / standards
  • Prospective Studies
  • Reference Values
  • Thyrotropin

Substances

  • Thyrotropin