Histamine Transmission Modulates the Phenotype of Murine Narcolepsy Caused by Orexin Neuron Deficiency

PLoS One. 2015 Oct 16;10(10):e0140520. doi: 10.1371/journal.pone.0140520. eCollection 2015.

Abstract

Narcolepsy type 1 is associated with loss of orexin neurons, sleep-wake derangements, cataplexy, and a wide spectrum of alterations in other physiological functions, including energy balance, cardiovascular, and respiratory control. It is unclear which narcolepsy signs are directly related to the lack of orexin neurons or are instead modulated by dysfunction of other neurotransmitter systems physiologically controlled by orexin neurons, such as the histamine system. To address this question, we tested whether some of narcolepsy signs would be detected in mice lacking histamine signaling (HDC-KO). Moreover, we studied double-mutant mice lacking both histamine signaling and orexin neurons (DM) to evaluate whether the absence of histamine signaling would modulate narcolepsy symptoms produced by orexin deficiency. Mice were instrumented with electrodes for recording the electroencephalogram and electromyogram and a telemetric arterial pressure transducer. Sleep attacks fragmenting wakefulness, cataplexy, excess rapid-eye-movement sleep (R) during the activity period, and enhanced increase of arterial pressure during R, which are hallmarks of narcolepsy in mice, did not occur in HDC-KO, whereas they were observed in DM mice. Thus, these narcolepsy signs are neither caused nor abrogated by the absence of histamine. Conversely, the lack of histamine produced obesity in HDC-KO and to a greater extent also in DM. Moreover, the regularity of breath duration during R was significantly increased in either HDC-KO or DM relative to that in congenic wild-type mice. Defects of histamine transmission may thus modulate the metabolic and respiratory phenotype of murine narcolepsy.

MeSH terms

  • Animals
  • Body Weight
  • Cardiovascular System / physiopathology
  • Cataplexy / metabolism
  • Cataplexy / pathology
  • Cataplexy / physiopathology
  • Energy Intake
  • Female
  • Gene Knockout Techniques
  • Histamine / metabolism*
  • Histidine Decarboxylase / deficiency
  • Histidine Decarboxylase / genetics
  • Male
  • Mice
  • Narcolepsy / metabolism*
  • Narcolepsy / pathology*
  • Neurons / metabolism*
  • Orexins / deficiency*
  • Phenotype*
  • Respiration
  • Signal Transduction*
  • Sleep
  • Wakefulness

Substances

  • Orexins
  • Histamine
  • Histidine Decarboxylase

Grants and funding

The authors received no specific funding for this work; they received founding from University of Bologna for general research activity.