Multiparameter flow cytometry is instrumental to distinguish myelodysplastic syndromes from non-neoplastic cytopenias

Eur J Cancer. 2016 Feb:54:49-56. doi: 10.1016/j.ejca.2015.11.013. Epub 2015 Dec 22.

Abstract

Mandatory for the diagnosis of myelodysplastic syndromes (MDS) is the presence of dysplasia in >10% of cells within one or more cell lineages or presence of >15% ring sideroblasts or presence of MDS-associated cytogenetic (CG) abnormalities. Discrimination between neo-plastic and non-neoplastic causes of cytopenias can be challenging when dysplastic features by cytomorphology (CM) are minimal and CG abnormalities are absent or non-discriminating from other myeloid neoplastic disorders. This study evaluated a standard diagnostic approach in 379 patients with unexplained cytopenias and highlights the additional value of flow cytometry (FC) in patients with indeterminate CM and CG. CM reached no clear-cut diagnosis in 44% of the patients. Here, CG was able to identify two additional patients with MDS; other CG results did not reveal abnormalities or were not contributory. Based on the FC results, patients without a diagnosis by CM and CG were categorized 'no MDS-related features' (65%), 'limited number of MDS-related changes' (24%), and 'consistent with MDS' (11%). Patients were followed over time in an attempt to establish or confirm a diagnosis (median follow-up 391 d, range 20-1764). The specificity (true negative) of MDS-FC analysis calculated after follow-up was 95%. FC can aid as a valuable tool to exclude MDS when CM and additional CG are not conclusive in patients with cytopenia.

Keywords: Cytopenias; Diagnosis; Flow cytometry; Myelodysplastic syndromes.

MeSH terms

  • Adult
  • Aged
  • Aged, 80 and over
  • Antigens, CD34 / analysis
  • Biomarkers / analysis
  • Bone Marrow Examination
  • Diagnosis, Differential
  • Female
  • Flow Cytometry / methods*
  • Humans
  • Immunophenotyping / methods*
  • Leukocyte Common Antigens / analysis
  • Leukopenia / diagnosis*
  • Leukopenia / etiology
  • Leukopenia / genetics
  • Leukopenia / immunology
  • Male
  • Middle Aged
  • Myelodysplastic Syndromes / complications
  • Myelodysplastic Syndromes / diagnosis*
  • Myelodysplastic Syndromes / genetics
  • Myelodysplastic Syndromes / immunology
  • Myeloid Progenitor Cells / immunology
  • Phenotype
  • Precursor Cells, B-Lymphoid / immunology
  • Predictive Value of Tests
  • Prognosis
  • Risk Factors
  • Time Factors
  • Young Adult

Substances

  • Antigens, CD34
  • Biomarkers
  • Leukocyte Common Antigens
  • PTPRC protein, human