We report a case of extra-adrenal retroperitoneal paraganglioma (RP) with extensive duodenal invasion and tumor thromboses both in the right testicular vein and in the inferior vena cava (IVC). Because there was rigid adherence between the RP and the abdominal aorta, pancreatoduodenectomy with replacement of the IVC and aorta was performed for complete surgical resection. In the present case, both the mode of progression of the RP and the surgical approach were extremely rare.
Keywords: Abdominal aortic replacement; Duodenal invasion; Inferior vena cava replacement; Inferior vena cava tumor thrombus; Pancreaticoduodenectomy; Paraganglioma.