IgG4-related systemic disease presenting with pleural effusion, ascites and dilated cardiomyopathy

Hee Jeong Lee; Hyoung Sul; Hyun Woo Kim; Young Sang Lyu; Chi Young Park; Ran Hong; Sang Gon Park

doi:10.5301/tj.5000502

IgG4-related systemic disease presenting with pleural effusion, ascites and dilated cardiomyopathy

Tumori. 2016 Nov 11;102(Suppl. 2). doi: 10.5301/tj.5000502.

Authors

Hee Jeong Lee¹, Hyoung Sul¹, Hyun Woo Kim¹, Young Sang Lyu¹, Chi Young Park¹, Ran Hong², Sang Gon Park¹

Affiliations

¹ Department of Internal Medicine, Chosun University Hospital, Gwangju - Republic of Korea.
² Department of Pathology, Chosun University Hospital, Gwangju - Republic of Korea.

PMID: 27079904
DOI: 10.5301/tj.5000502

Abstract

Purpose: We report the case of a patient with IgG4-related disease with multiple organ involvement, especially myocardium, that was successfully treated with prednisone.

Methods: We performed several serological tests, electrocardiogram, echocardiography, computed tomography and inguinal lymph node biopsy.

Results: We diagnosed the patient with IgG4-related disease by the elevated serum IgG4 level and histological lymph node findings.

Conclusions: This is the first reported case of IgG4-related disease with dilated cardiomyopathy.

Publication types

Case Reports

MeSH terms

Adult
Ascites / diagnosis
Ascites / drug therapy
Ascites / immunology*
Biopsy
Cardiomyopathy, Dilated / diagnosis*
Cardiomyopathy, Dilated / drug therapy
Cardiomyopathy, Dilated / immunology*
Electrocardiography
Humans
Immunoglobulin G / blood
Immunoglobulin G / immunology*
Lymph Nodes / pathology
Male
Pleural Effusion / diagnosis
Pleural Effusion / drug therapy
Pleural Effusion / immunology*
Prednisone / administration & dosage
Prednisone / therapeutic use
Radiography, Thoracic
Tomography, X-Ray Computed
Treatment Outcome

Substances

Immunoglobulin G
Prednisone