Calcium/calmodulin-dependent kinase kinase 2 regulates hematopoietic stem and progenitor cell regeneration

Cell Death Dis. 2017 Oct 5;8(10):e3076. doi: 10.1038/cddis.2017.474.

Abstract

Hematopoietic stem and progenitor cells (HSPCs) are predominantly quiescent in adults, but proliferate in response to bone marrow (BM) injury. Here, we show that deletion of Ca2+/calmodulin (CaM)-dependent protein kinase kinase 2 (CaMKK2) promotes HSPC regeneration and hematopoietic recovery following radiation injury. Using Camkk2-enhanced green fluorescent protein (EGFP) reporter mice, we found that Camkk2 expression is developmentally regulated in HSPC. Deletion of Camkk2 in HSPC results in a significant downregulation of genes affiliated with the quiescent signature. Accordingly, HSPC from Camkk2 null mice have a high proliferative capability when stimulated in vitro in the presence of BM-derived endothelial cells. In addition, Camkk2 null mice are more resistant to radiation injury and show accelerated hematopoietic recovery, enhanced HSPC regeneration and ultimately a prolonged survival following sublethal or lethal total body irradiation. Mechanistically, we propose that CaMKK2 regulates the HSPC response to hematopoietic damage by coupling radiation signaling to activation of the anti-proliferative AMP-activated protein kinase. Finally, we demonstrated that systemic administration of the small molecule CaMKK2 inhibitor, STO-609, to irradiated mice enhanced HSPC recovery and improved survival. These findings identify CaMKK2 as an important regulator of HSPC regeneration and demonstrate CaMKK2 inhibition is a novel approach to promoting hematopoietic recovery after BM injury.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Animals
  • Benzimidazoles / administration & dosage
  • Calcium / metabolism
  • Calcium-Calmodulin-Dependent Protein Kinase Kinase / genetics*
  • Calmodulin / genetics*
  • Green Fluorescent Proteins / genetics
  • Hematopoietic Stem Cells / metabolism*
  • Mice
  • Mice, Knockout
  • Naphthalimides / administration & dosage
  • Radiation Injuries / drug therapy*
  • Radiation Injuries / genetics
  • Radiation Injuries / pathology
  • Regeneration / genetics
  • Signal Transduction / drug effects
  • Whole-Body Irradiation

Substances

  • Benzimidazoles
  • Calmodulin
  • Naphthalimides
  • STO 609
  • Green Fluorescent Proteins
  • Calcium-Calmodulin-Dependent Protein Kinase Kinase
  • Camkk2 protein, mouse
  • Calcium