The E3 ligases Itch and WWP2 cooperate to limit TH2 differentiation by enhancing signaling through the TCR

Nat Immunol. 2018 Jul;19(7):766-775. doi: 10.1038/s41590-018-0137-8. Epub 2018 Jun 20.

Abstract

The mechanisms by which the sensitivity of naive CD4+ T cells to stimulation by the cognate antigen via the T cell antigen receptor (TCR) determines their differentiation into distinct helper T cell subsets remain elusive. Here we demonstrate functional collaboration of the ubiquitin E3 ligases Itch and WWP2 in regulating the strength of the TCR signal. Mice lacking both Itch and WWP2 in T cells showed spontaneous autoimmunity and lung inflammation. CD4+ T cells deficient in Itch and WWP2 exhibited hypo-responsiveness to TCR stimulation and a bias toward differentiation into the TH2 subset of helper T cells. Itch and WWP2 formed a complex and cooperated to enhance TCR-proximal signaling by catalyzing the conjugation of atypical ubiquitin chains to the phosphatase SHP-1 and reducing the association of SHP-1 with the tyrosine kinase Lck. These findings indicate that targeted ubiquitination regulates the strength of the TCR signal and differentiation toward the TH2 lineage.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Autoimmunity
  • Cell Differentiation
  • Humans
  • Inflammation / genetics
  • Jurkat Cells
  • Lymphocyte Specific Protein Tyrosine Kinase p56(lck) / metabolism
  • Mice
  • Mice, Knockout
  • Protein Tyrosine Phosphatase, Non-Receptor Type 6 / metabolism
  • Receptors, Antigen, T-Cell / metabolism*
  • Repressor Proteins / metabolism
  • Signal Transduction
  • Th2 Cells / enzymology
  • Th2 Cells / immunology*
  • Ubiquitin-Protein Ligases / genetics
  • Ubiquitin-Protein Ligases / metabolism
  • Ubiquitin-Protein Ligases / physiology*
  • Ubiquitination

Substances

  • Receptors, Antigen, T-Cell
  • Repressor Proteins
  • ITCH protein, human
  • Itch protein, mouse
  • WWP2 protein, human
  • Wwp2 protein, mouse
  • Ubiquitin-Protein Ligases
  • Lymphocyte Specific Protein Tyrosine Kinase p56(lck)
  • Protein Tyrosine Phosphatase, Non-Receptor Type 6