Developmental processes regulate craniofacial variation in disease and evolution

Genesis. 2019 Jan;57(1):e23249. doi: 10.1002/dvg.23249. Epub 2018 Oct 1.

Abstract

Variation in development mediates phenotypic differences observed in evolution and disease. Although the mechanisms underlying phenotypic variation are still largely unknown, recent research suggests that variation in developmental processes may play a key role. Developmental processes mediate genotype-phenotype relationships and consequently play an important role regulating phenotypes. In this review, we provide an example of how shared and interacting developmental processes may explain convergence of phenotypes in spliceosomopathies and ribosomopathies. These data also suggest a shared pathway to disease treatment. We then discuss three major mechanisms that contribute to variation in developmental processes: genetic background (gene-gene interactions), gene-environment interactions, and developmental stochasticity. Finally, we comment on evolutionary alterations to developmental processes, and the evolution of disease buffering mechanisms.

Keywords: craniofacial anomalies; evolution of development; genotype-phenotype relationships; morphological variation; ribosomopathies; spliceosomopathies.

Publication types

  • Research Support, N.I.H., Extramural
  • Review

MeSH terms

  • Animals
  • Bone Development / genetics*
  • Craniofacial Dysostosis / genetics*
  • Craniofacial Dysostosis / metabolism
  • Evolution, Molecular*
  • Gene Expression Regulation, Developmental*
  • Humans
  • RNA Splicing
  • Ribosomes / genetics
  • Skull / embryology
  • Skull / metabolism