Isolated Congenital Dysgenesia of a Pulmonary Valve Cusp Presenting as a Pulmonary Artery Aneurysm

Ann Thorac Surg. 2019 Jun;107(6):e385-e387. doi: 10.1016/j.athoracsur.2018.10.030. Epub 2018 Nov 23.

Abstract

Pulmonary artery aneurysm is a rare disorder, with the underlying pathology remaining obscure in many instances. More common causes include pulmonary hypertension, poststenotic dilation, or vasculitis. In this case series, we report 3 patients presenting with isolated pulmonary artery aneurysms in whom multimodality imaging revealed the dysgenesia of a single pulmonary valve cusp as the cause of the huge pulmonary aneurysm.

Publication types

  • Case Reports

MeSH terms

  • Aneurysm / etiology*
  • Female
  • Humans
  • Middle Aged
  • Pulmonary Artery*
  • Pulmonary Valve / abnormalities*
  • Young Adult