Incidence of inhibitors in patients with severe and moderate hemophilia A treated with factor VIII concentrates

Am J Hematol. 1987 Mar;24(3):241-5. doi: 10.1002/ajh.2830240303.

Abstract

Recent data published on the prevalence of inhibitors to factor VIII in hemophiliacs on treatment show great variations, with prevalence rates ranging from 3.6 to 14.2%. We have studied the cumulative risk of inhibitor development in a cohort of 62 patients with hemophilia A. All patients were born after 1960, were natives of the Vienna area, had a factor VIII activity of less than 5%, and were treated at least once. Using the method of Cutler and Ederer, the cumulative risk of inhibitor development was found to be 24% at the age of 25 years. Most inhibitors developed between the ages of 3 and 7 years. The current prevalence of F VIII inhibitors in the group of patients studied is 17.5%. It is concluded that prevalence data underestimate the true risk of inhibitor development.

MeSH terms

  • Adult
  • Factor VIII / antagonists & inhibitors*
  • Factor VIII / therapeutic use
  • Hemophilia A / blood*
  • Hemophilia A / drug therapy
  • Hemophilia A / mortality
  • Humans

Substances

  • Factor VIII