[Pseudotumoral calcinosis of the wrist compressing the radial nerve in systemic sclerosis]

Ann Dermatol Venereol. 2020 May;147(5):366-369. doi: 10.1016/j.annder.2019.09.612. Epub 2020 Jan 15.
[Article in French]

Abstract

Background: Pseudotumoral calcinosis, a rare complication of systemic scleroderma, is characterized by the presence in extra-articular tissue, but rarely intra-articular tissue, of large masses made up of hydroxyapatite crystals.

Patients and methods: We report an original case of intra- and extra-articular pseudotumoral calcinosis of the wrist diagnosed in a patient followed for mild systemic scleroderma. The calcinosis was revealed in a highly unusual way via ductal syndrome secondary to compression of the radial nerve in the wrist. Surgical treatment resulted in marked clinical and functional improvement.

Comment: Although subcutaneous calcinoses are a fairly common complication of systemic scleroderma, the pseudo-tumoral form remains extremely rare. It may be complicated by pain, recurrent infection, and functional restriction, but literature contains only very rare reports of its revelation via ductal syndrome.

Keywords: Calcinose pseudo-tumorale; Ductal syndrome; Nerf radial; Pseudotumoral calcinosis; Radial nerve; Sclérodermie systémique; Syndrome canalaire; Systemic sclerosis.

Publication types

  • Case Reports

MeSH terms

  • Calcinosis / complications
  • Calcinosis / etiology*
  • Female
  • Humans
  • Middle Aged
  • Nerve Compression Syndromes / etiology*
  • Radial Nerve*
  • Scleroderma, Systemic / complications*
  • Wrist*