Concealed congenital long QT syndrome during velopharyngeal dysfunction correction: a case report

J Dent Anesth Pain Med. 2020 Jun;20(3):165-171. doi: 10.17245/jdapm.2020.20.3.165. Epub 2020 Jun 24.

Abstract

The congenital long QT syndrome (LQTS) is an inherited cardiac disorder characterized by increased QT intervals and a tendency to experience ventricular tachycardia, which can cause fainting, heart failure, or sudden death. A 4-year-old female patient undergoing velopharyngeal correction surgery under general anesthesia suddenly developed Torsades de pointes. Although the patient spontaneously resolved to sinus rhythm without treatment, subsequent QT prolongation persisted. Here, we report a case of concealed LQTS with a literature review.

Keywords: Electrocardiogram; Long QT Syndrome; Torsades de Pointes.

Publication types

  • Case Reports