ATR is essential for preservation of cell mechanics and nuclear integrity during interstitial migration

Nat Commun. 2020 Sep 24;11(1):4828. doi: 10.1038/s41467-020-18580-9.

Abstract

ATR responds to mechanical stress at the nuclear envelope and mediates envelope-associated repair of aberrant topological DNA states. By combining microscopy, electron microscopic analysis, biophysical and in vivo models, we report that ATR-defective cells exhibit altered nuclear plasticity and YAP delocalization. When subjected to mechanical stress or undergoing interstitial migration, ATR-defective nuclei collapse accumulating nuclear envelope ruptures and perinuclear cGAS, which indicate loss of nuclear envelope integrity, and aberrant perinuclear chromatin status. ATR-defective cells also are defective in neuronal migration during development and in metastatic dissemination from circulating tumor cells. Our findings indicate that ATR ensures mechanical coupling of the cytoskeleton to the nuclear envelope and accompanying regulation of envelope-chromosome association. Thus the repertoire of ATR-regulated biological processes extends well beyond its canonical role in triggering biochemical implementation of the DNA damage response.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Actin Cytoskeleton
  • Animals
  • Ataxia Telangiectasia Mutated Proteins / genetics
  • Ataxia Telangiectasia Mutated Proteins / metabolism*
  • Brain
  • Cell Nucleus / metabolism*
  • Chromatin
  • Cytoplasm
  • Cytoskeleton / metabolism
  • DNA Damage
  • Mice, Knockout
  • Neoplasm Metastasis
  • Neurogenesis
  • Nuclear Envelope / metabolism
  • Stress, Mechanical*

Substances

  • Chromatin
  • ATR protein, human
  • Ataxia Telangiectasia Mutated Proteins