BCL-XL exerts a protective role against anemia caused by radiation-induced kidney damage

EMBO J. 2020 Dec 15;39(24):e105561. doi: 10.15252/embj.2020105561. Epub 2020 Nov 25.

Abstract

Studies of gene-targeted mice identified the roles of the different pro-survival BCL-2 proteins during embryogenesis. However, little is known about the role(s) of these proteins in adults in response to cytotoxic stresses, such as treatment with anti-cancer agents. We investigated the role of BCL-XL in adult mice using a strategy where prior bone marrow transplantation allowed for loss of BCL-XL exclusively in non-hematopoietic tissues to prevent anemia caused by BCL-XL deficiency in erythroid cells. Unexpectedly, the combination of total body γ-irradiation (TBI) and genetic loss of Bcl-x caused secondary anemia resulting from chronic renal failure due to apoptosis of renal tubular epithelium with secondary obstructive nephropathy. These findings identify a critical protective role of BCL-XL in the adult kidney and inform on the use of BCL-XL inhibitors in combination with DNA damage-inducing drugs for cancer therapy. Encouragingly, the combination of DNA damage-inducing anti-cancer therapy plus a BCL-XL inhibitor could be tolerated in mice, at least when applied sequentially.

Keywords: BCL-XL; BH3-mimetic drugs; DNA damage; apoptosis; kidney failure.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Anemia / prevention & control*
  • Animals
  • Antineoplastic Agents / pharmacology
  • Apoptosis / drug effects
  • Apoptosis Regulatory Proteins / genetics
  • Bcl-2-Like Protein 11 / genetics
  • DNA Damage
  • Female
  • Gamma Rays
  • Hematologic Neoplasms / pathology
  • Inflammation
  • Kidney / metabolism
  • Kidney / pathology
  • Kidney / radiation effects*
  • Liver / pathology
  • Male
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • Proto-Oncogene Proteins c-bcl-2 / genetics
  • Proto-Oncogene Proteins c-bcl-2 / metabolism
  • Transcriptome
  • Tumor Suppressor Proteins / genetics
  • bcl-X Protein / deficiency
  • bcl-X Protein / genetics
  • bcl-X Protein / metabolism*
  • bcl-X Protein / pharmacology*

Substances

  • Antineoplastic Agents
  • Apoptosis Regulatory Proteins
  • Bcl-2-Like Protein 11
  • Bcl2l1 protein, mouse
  • Bcl2l11 protein, mouse
  • PUMA protein, mouse
  • Proto-Oncogene Proteins c-bcl-2
  • Tumor Suppressor Proteins
  • bcl-X Protein