Catalysis of proline isomerization and molecular chaperone activity in a tug-of-war

Nat Commun. 2020 Nov 27;11(1):6046. doi: 10.1038/s41467-020-19844-0.

Abstract

Catalysis of cis/trans isomerization of prolines is important for the activity and misfolding of intrinsically disordered proteins. Catalysis is achieved by peptidylprolyl isomerases, a superfamily of molecular chaperones. Here, we provide atomic insight into a tug-of-war between cis/trans isomerization and molecular chaperone activity. Catalysis of proline isomerization by cyclophilin A lowers the energy barrier for α-synuclein misfolding, while isomerase-binding to a separate, disease-associated protein region opposes aggregation. We further show that cis/trans isomerization outpowers the holding activity of cyclophilin A. Removal of the proline isomerization barrier through posttranslational truncation of α-synuclein reverses the action of the proline isomerase and turns it into a potent molecular chaperone that inhibits protein misfolding. The data reveal a conserved mechanism of dual functionality in cis/trans isomerases and define its molecular determinants acting on intrinsically disordered proteins.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amyloid / chemistry
  • Catalysis
  • Cyclophilin A / chemistry
  • Cyclophilin A / metabolism
  • Cyclosporine / pharmacology
  • Humans
  • Isomerism
  • Kinetics
  • Magnetic Resonance Spectroscopy
  • Models, Molecular
  • Molecular Chaperones / metabolism*
  • Parkinson Disease / metabolism
  • Proline / chemistry*
  • Proline / metabolism*
  • Protein Aggregates
  • Protein Binding
  • Protein Domains
  • alpha-Synuclein / chemistry
  • alpha-Synuclein / metabolism

Substances

  • Amyloid
  • Molecular Chaperones
  • Protein Aggregates
  • alpha-Synuclein
  • Cyclosporine
  • Proline
  • Cyclophilin A