[Clinical phenotype and genetic analysis of a child with 3p26.3p25.3 deletion]

Zhonghua Yi Xue Yi Chuan Xue Za Zhi. 2023 Feb 10;40(2):234-237. doi: 10.3760/cma.j.cn511393-20220412-00247.
[Article in Chinese]

Abstract

Objective: To explore the genetic basis for a child with facial dysmorphism and multiple malformations.

Methods: The child, born at 34+6 weeks' gestation due to premature rupture of amniotic membrane, dichorionic diamniotic twinning and gestational diabetes, was subjected to chromosomal karyotyping analysis and copy number variations sequencing (CNV-seq).

Results: The child was found to have facial dysmorphism, hypospadia, cryptorchidism and hypotonia. He was found to have a 46,XY,del(3)(p26) karyotype in addition with a 9.80 Mb deletion (chr3: 60 000-9 860 000) encompassing 33 protein coding genes.

Conclusion: The 3p26.3p25.3 deletion probably underlay the multiple malformations in this child. Continuous follow-up is required to improve his quality of life.

Publication types

  • English Abstract

MeSH terms

  • Abnormalities, Multiple* / genetics
  • Chromosome Deletion*
  • DNA Copy Number Variations
  • Humans
  • Male
  • Phenotype
  • Quality of Life