Serine-129 phosphorylation of α-synuclein is an activity-dependent trigger for physiologic protein-protein interactions and synaptic function

Neuron. 2023 Dec 20;111(24):4006-4023.e10. doi: 10.1016/j.neuron.2023.11.020.

Abstract

Phosphorylation of α-synuclein at the serine-129 site (α-syn Ser129P) is an established pathologic hallmark of synucleinopathies and a therapeutic target. In physiologic states, only a fraction of α-syn is phosphorylated at this site, and most studies have focused on the pathologic roles of this post-translational modification. We found that unlike wild-type (WT) α-syn, which is widely expressed throughout the brain, the overall pattern of α-syn Ser129P is restricted, suggesting intrinsic regulation. Surprisingly, preventing Ser129P blocked activity-dependent synaptic attenuation by α-syn-thought to reflect its normal function. Exploring mechanisms, we found that neuronal activity augments Ser129P, which is a trigger for protein-protein interactions that are necessary for mediating α-syn function at the synapse. AlphaFold2-driven modeling and membrane-binding simulations suggest a scenario where Ser129P induces conformational changes that facilitate interactions with binding partners. Our experiments offer a new conceptual platform for investigating the role of Ser129 in synucleinopathies, with implications for drug development.

Keywords: AlphaFold; CRISPR; alanine mutations; endogenous tagging; neuronal activity; pHluorin; proximity-ligation assay; serine phosphorylation; synapses; α-synuclein.

MeSH terms

  • Humans
  • Parkinson Disease* / metabolism
  • Phosphorylation
  • Serine / metabolism
  • Synucleinopathies*
  • alpha-Synuclein / metabolism

Substances

  • alpha-Synuclein
  • Serine