Growth in children with nephrotic syndrome: a post hoc analysis of the NEPTUNE study

Pediatr Nephrol. 2024 Sep;39(9):2691-2701. doi: 10.1007/s00467-024-06375-9. Epub 2024 Apr 26.

Abstract

Background: Steroids, the mainstay of treatment for nephrotic syndrome in children, have multiple adverse effects including growth suppression.

Methods: Anthropometric measurements in children < 18 years enrolled in the Nephrotic Syndrome Study Network (NEPTUNE) were collected. The longitudinal association of medication exposure and nephrotic syndrome characteristics with height z-score and growth velocity was determined using adjusted Generalized Estimating Equation regression and linear regression.

Results: A total of 318 children (57.2% males) with a baseline age of 7.64 ± 5.04 years were analyzed. The cumulative steroid dose was 216.4 (IQR 61.5, 652.7) mg/kg (N = 233). Overall, height z-scores were not significantly different at the last follow-up compared to baseline (- 0.13 ± 1.21 vs. - 0.23 ± 1.71, p = 0.21). In models adjusted for age, sex, and eGFR, greater cumulative steroid exposure (β - 7.5 × 10-6, CI - 1.2 × 10-5, - 3 × 10-6, p = 0.001) and incident cases of NS (vs. prevalent) (β - 1.1, CI - 2.22, - 0.11, p = 0.03) were significantly associated with lower height z-scores over time. Rituximab exposure was associated with higher height z-scores (β 0.16, CI 0.04, 0.29, p = 0.01) over time.

Conclusion: Steroid dose was associated with lower height z-score, while rituximab use was associated with higher height z-score.

Keywords: Body mass index (BMI); Height; Nephrotic syndrome; Steroids; Weight.

Publication types

  • Multicenter Study

MeSH terms

  • Adolescent
  • Body Height* / drug effects
  • Child
  • Child, Preschool
  • Female
  • Glucocorticoids / administration & dosage
  • Glucocorticoids / adverse effects
  • Glucocorticoids / therapeutic use
  • Growth Disorders / diagnosis
  • Growth Disorders / drug therapy
  • Growth Disorders / etiology
  • Humans
  • Longitudinal Studies
  • Male
  • Nephrotic Syndrome* / drug therapy
  • Rituximab / administration & dosage
  • Rituximab / adverse effects

Substances

  • Glucocorticoids
  • Rituximab